一例原发性睾丸横纹肌肉瘤患儿病例。

A case of children with primary intratesticular rhabdomyosarcoma.

作者信息

Majid Ghani Ikhsan, Rachmadiyan Alyadi, Octavian Irvan, Karim M Ilhamul, Mardianty Friska

机构信息

Department of Urology, Cibabat Regional General Hospital, Cimahi, West Java, Indonesia.

Pathology Laboratory, Hermina Arcamanik Hospital, Bandung, West Java, Indonesia.

出版信息

Urol Case Rep. 2022 Nov 30;46:102293. doi: 10.1016/j.eucr.2022.102293. eCollection 2023 Jan.

DOI:10.1016/j.eucr.2022.102293

PMID:36478963

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9720432/

Abstract

In children, the most typical soft tissue tumor is a rhabdomyosarcoma (RMS). A primary intratesticular rhabdomyosarcoma is quite uncommon. An eleven-year-old had a painless left testicular tumor for two months. The patient's left scrotum was found to have a firm, non-tender lump. A massive hypoechoic intratesticular mass measuring 8.0 × 7.5 × 6.0 cm was found in the left scrotum by scrotal and abdominal ultrasonography. The patient had an inguinal orchiectomy. Histopathological examination disclosed botryoid rhabdomyosarcoma. Primary intratesticular rhabdomyosarcomas are rare. Radical orchiectomy and chemotherapy are recommended. It may increase overall and disease-free survival.

摘要

在儿童中，最典型的软组织肿瘤是横纹肌肉瘤（RMS）。原发性睾丸内横纹肌肉瘤相当罕见。一名11岁儿童左侧睾丸无痛性肿物已有两个月。发现患者左侧阴囊有一个质地坚硬、无压痛的肿块。通过阴囊及腹部超声检查，在左侧阴囊发现一个8.0×7.5×6.0厘米的巨大低回声睾丸内肿物。患者接受了腹股沟睾丸切除术。组织病理学检查显示为葡萄状横纹肌肉瘤。原发性睾丸内横纹肌肉瘤很罕见。推荐行根治性睾丸切除术及化疗。这可能会提高总生存率和无病生存率。