Fukami Kumiko, Furihata Makoto, Yano Shintaro, Okawa Hiroki, Nishi Shinjiro, Nakatsu Yoichi, Nomoto Yusuke, Ogiwara Shingo, Kitamura Tsuneo, Tomita Shigeki, Osada Taro
Department of Gastroenterology, Juntendo University Urayasu Hospital, Urayasu-shi, Chiba, Japan.
Department of Pathology, Juntendo University Urayasu Hospital, Urayasu-shi, Chiba, Japan.
ACG Case Rep J. 2022 Dec 26;9(12):e00936. doi: 10.14309/crj.0000000000000936. eCollection 2022 Dec.
Juvenile polyps (JPs) are common, developing mostly as solitary, hamartomatous lesions in the colorectum, and principally affect pediatric patients. Solitary JPs are recognized as benign, with a negligible malignant transformation rate. Primary signet ring cell carcinoma is a rare type of colorectal cancer (0.1%-2.6%) that presents mostly at an advanced stage in younger patients and affects the right-sided colon, with extensive lymphatic invasion and peritoneal dissemination, resulting in a poorer prognosis compared with conventional colorectal cancer. We report a rare case of signet ring cell carcinoma in a solitary JP treated with endoscopic mucosal resection.
幼年性息肉(JPs)很常见,大多表现为结直肠内单发的错构瘤性病变,主要影响儿科患者。单发幼年性息肉被认为是良性的,恶变率可忽略不计。原发性印戒细胞癌是一种罕见的结直肠癌类型(0.1%-2.6%),多见于年轻患者的晚期,累及右半结肠,伴有广泛的淋巴侵犯和腹膜播散,与传统结直肠癌相比预后较差。我们报告了1例经内镜黏膜切除术治疗的单发幼年性息肉并发印戒细胞癌的罕见病例。