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结节病罕见的骨定位表现类似转移瘤:病例报告及文献复习

Unusual bone localization of sarcoidosis mimicking metastatic lesions: case report and review of literature.

作者信息

Hamdi Besma, Ben Jemia Emna, Attia Monia, Khalfallah Ikbel, Riahi Hend, Berraies Anissa, Ladeb Mohamed Faouzi, Rammeh Soumaya, Hamzaoui Agnes

机构信息

Pulmonology Departement Diseases, Abderrahmen Mami Hospital, Ariana 2080, Tunisia.

University of Tunis El Manar, Faculty of Medicine of Tunis, Tunis 1007, Tunisia.

出版信息

Sarcoidosis Vasc Diffuse Lung Dis. 2022;39(3):e2022034. doi: 10.36141/svdld.v39i3.8744. Epub 2022 Sep 23.

Abstract

Sarcoidosis is a multisystem disease of unknown origin. Diagnosis remains challenging, based on organ site involvement, histological confirmation of non-caseating granuloma and an appropriate clinical syndrome. Granulomatous bone involvement is rare and may be ignored because it is usually asymptomatic. Vertebrae, ribs and skull localizations are rarely reported. We described an interesting case of a woman with chronic and multiorgan sarcoidosis with unusual bone localizations.

摘要

结节病是一种病因不明的多系统疾病。基于器官部位受累情况、非干酪样肉芽肿的组织学证实以及适当的临床综合征,诊断仍然具有挑战性。肉芽肿性骨受累较为罕见,且通常无症状,可能会被忽视。很少有关于脊椎、肋骨和颅骨受累部位的报道。我们描述了一例有趣的病例,一名患有慢性多器官结节病且伴有不寻常骨受累部位的女性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ce06/9766854/e7124c5abaa9/SVDLD-39-34-g001.jpg

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