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乙状结肠扭转梗阻:溃疡性结肠炎患儿的一种罕见并发症。

Obstructing Sigmoid Volvulus: An Unusual Complication in a Pediatric Patient With Ulcerative Colitis.

作者信息

Mittal Aditi, DeRoss Anthony, Goldman Deborah, Chen Charles B, Kay Marsha

机构信息

Department of Pediatric Gastroenterology, Hepatology and Nutrition, Cleveland Clinic Children's, Cleveland, OH.

Department of Pediatric Surgery, Cleveland Clinic Children's, Cleveland, OH.

出版信息

ACG Case Rep J. 2023 Mar 2;10(2):e00998. doi: 10.14309/crj.0000000000000998. eCollection 2023 Feb.

DOI:10.14309/crj.0000000000000998
PMID:36876286
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9981391/
Abstract

Acute colonic dilation in pediatric patients with ulcerative colitis (UC) raises a concern for toxic megacolon, but other rare conditions such as sigmoid volvulus may present in a similar manner. We report a rare case of a teenager with UC without prior surgery who developed an obstructing sigmoid volvulus managed with endoscopic detorsion and decompression. Colonic inflammation in patients with UC may result in a volvulus in the absence of other predisposing factors and should be considered in the differential diagnosis of patients with UC who present with obstructive symptoms with an atypical presentation.

摘要

溃疡性结肠炎(UC)患儿出现急性结肠扩张会引发中毒性巨结肠的担忧,但其他罕见情况如乙状结肠扭转也可能以类似方式表现。我们报告了一例罕见病例,一名未曾接受过手术的青少年溃疡性结肠炎患者发生了梗阻性乙状结肠扭转,通过内镜扭转复位和减压进行治疗。在没有其他易感因素的情况下,溃疡性结肠炎患者的结肠炎症可能导致扭转,对于出现梗阻症状且表现不典型的溃疡性结肠炎患者,鉴别诊断时应考虑到这一点。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/73bf7b12f0fc/ac9-10-e00998-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/03fb10128cc5/ac9-10-e00998-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/623db11aff61/ac9-10-e00998-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/7ea56d5f5db7/ac9-10-e00998-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/a6cb24d309a3/ac9-10-e00998-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/73bf7b12f0fc/ac9-10-e00998-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/03fb10128cc5/ac9-10-e00998-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/623db11aff61/ac9-10-e00998-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/7ea56d5f5db7/ac9-10-e00998-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/a6cb24d309a3/ac9-10-e00998-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/326f/9981391/73bf7b12f0fc/ac9-10-e00998-g005.jpg

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本文引用的文献

1
Sigmoid volvulus in children.儿童乙状结肠扭转
BMJ Case Rep. 2021 May 12;14(5):e241869. doi: 10.1136/bcr-2021-241869.
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A case report and literature review of sigmoid volvulus in children.儿童乙状结肠扭转的病例报告及文献综述
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Endoscopic management of sigmoid volvulus in children.儿童乙状结肠扭转的内镜治疗
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Presentation and endoscopic management of sigmoid volvulus in children.儿童乙状结肠扭转的临床表现及内镜治疗
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The twisted colon: a review of sigmoid volvulus.扭曲的结肠:乙状结肠扭转综述
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Toxic megacolon.中毒性巨结肠。
Inflamm Bowel Dis. 2012 Mar;18(3):584-91. doi: 10.1002/ibd.21847.
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Non-toxic megacolon due to transverse and sigmoid colon volvulus in a patient with ulcerative colitis.因溃疡性结肠炎导致的横结肠和乙状结肠扭转而出现非毒性巨结肠。
J Crohns Colitis. 2009 Feb;3(1):38-41. doi: 10.1016/j.crohns.2008.09.002. Epub 2008 Oct 26.
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Crohn disease of the small bowel: comparison of CT enterography, MR enterography, and small-bowel follow-through as diagnostic techniques.小肠克罗恩病:CT小肠造影、磁共振小肠造影和小肠钡剂造影作为诊断技术的比较
Radiology. 2009 Jun;251(3):751-61. doi: 10.1148/radiol.2513081184. Epub 2009 Mar 10.
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Definition of phenotypic characteristics of childhood-onset inflammatory bowel disease.儿童期起病的炎症性肠病的表型特征定义。
Gastroenterology. 2008 Oct;135(4):1114-22. doi: 10.1053/j.gastro.2008.06.081. Epub 2008 Jul 3.
10
Crohn's disease: factors associated with exposure to high levels of diagnostic radiation.克罗恩病:与高剂量诊断性辐射暴露相关的因素
Gut. 2008 Nov;57(11):1524-9. doi: 10.1136/gut.2008.151415. Epub 2008 Apr 28.