Reding R, Claus D, Kestens P J, Otte J B
Cliniques Universitaires St-Luc, Bruxelles, Belgique.
Chir Pediatr. 1987;28(3):145-50.
Congenital cystic dilatation of the common bile duct, also known as choledochal cyst, is an uncommon malformation, observed mainly in asiatic children, with a 3:1 female--male ratio. The entity is classified into 4 different types according to the anatomy of the malformation, which effects or not the intrahepatic biliary tree. The authors review theirs experience with 16 consecutive patients with choledochal cyst operated between 1971 and 1985. In 12 children (mean age: 5,8 years, 11 girls) without previous surgery, preoperative diagnosis was made with abdominal ultrasonography and, in some cases, endoscopic retrograde cholangio-wirsungography. Peroperative cholangiography demonstrated a common pancreatico-biliary channel associated with high choledochal amylase content in 6 cases. Surgical treatment consisted in cyst excision with hepatico-jejunostomy in those 12 patients. We also discuss the surgical treatment of 4 previously operated patients with postoperative cholangitis or biliary carcinoma. An anomalous pancreatico-biliary ductal junction (long common channel allowing free pancreatico-biliary reflux) is usually observed in these patients; it is considered to play a role in the etiology of congenital choledochal cysts. Appropriate surgical treatment consists in cyst excision with hepatico-jejunostomy as biliary drainage, in order to eliminate bile stasis, to remove the mechanism which allows continuous pancreatico-biliary reflux and to prevent the occurrence of bile duct carcinoma.
先天性胆总管囊肿,又称胆管囊肿,是一种罕见的畸形,主要见于亚洲儿童,男女比例为3:1。根据畸形的解剖结构,该疾病可分为4种不同类型,其可累及或不累及肝内胆管树。作者回顾了1971年至1985年间连续收治的16例胆管囊肿患者的治疗经验。在12例未接受过手术的儿童(平均年龄:5.8岁,11名女孩)中,术前通过腹部超声检查进行诊断,部分病例还进行了内镜逆行胰胆管造影。术中胆管造影显示6例患者存在胰胆管共同通道,且胆总管淀粉酶含量升高。这12例患者的手术治疗包括囊肿切除及肝空肠吻合术。我们还讨论了4例曾接受过手术的患者术后胆管炎或胆管癌的手术治疗。这些患者通常存在异常的胰胆管汇合(长的共同通道允许胰胆管自由反流);其被认为在先天性胆管囊肿的病因学中起作用。合适的手术治疗包括囊肿切除及肝空肠吻合术作为胆汁引流,以消除胆汁淤积,消除允许持续胰胆管反流的机制,并预防胆管癌的发生。