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皮肌炎合并胸腺瘤:一例报告及文献复习

Dermatomyositis associated with thymoma: A case report and literature review.

作者信息

Yıldırım F, Mutlu M Y, İçaçan O C, Bes C

机构信息

University of Health Sciences, Başakşehir Çam and Sakura City Hospital, Department of Rheumatology, İstanbul, TURKEY.

出版信息

Clin Ter. 2023 Mar-Apr;174(2):115-120. doi: 10.7417/CT.2023.2506.

Abstract

Thymoma can present with paraneoplastic-autoimmune neuro-muscular disorders, including polymyositis, dermatomyositis, and granulomatous myositis. Rarely, concomitant subclinical myasthenia gravis (MG) can be a diagnostic dilemma and cause deleterious outcomes regarding missed or delayed diagnosis. We report a Turkish patient presented with thymoma associated dermatomyositis and positive acetylcholine receptor antibody without evident MG clinic.

摘要

胸腺瘤可伴发副肿瘤性自身免疫性神经肌肉疾病,包括多发性肌炎、皮肌炎和肉芽肿性肌炎。罕见的是,合并亚临床重症肌无力(MG)可能会成为诊断难题,并因漏诊或诊断延迟而导致不良后果。我们报告了一名土耳其患者,该患者表现为胸腺瘤相关皮肌炎且乙酰胆碱受体抗体阳性,但无明显MG临床表现。

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