Rheumatology Clinic, University Hospital St. Marina, Varna, 9010, Bulgaria.
First Department of Internal Medicine, Faculty of Medicine, Medical University-Varna, Varna, Bulgaria.
Rheumatol Int. 2023 May;43(5):975-981. doi: 10.1007/s00296-023-05309-2. Epub 2023 Mar 15.
Takayasu's arteritis (TA) is a chronic granulomatous vasculitis that predominantly affects the aorta and its major branches. Despite advancements in the understanding of the pathogenic pathways of vascular inflammation, the etiology and predisposing factors of TA remain to be fully understood. In susceptible individuals, exposure to adjuvants may trigger, unlock or unmask an autoimmune disorder, presenting as non-specific constitutional symptoms or a fully developed autoimmune syndrome such as vasculitis. Here, we hypothesize that TA could be triggered by siliconosis, a subtype of the autoimmune/inflammatory syndrome induced by adjuvants (ASIA). ASIA, also known as Shoenfeld syndrome, encompasses a wide range of autoimmune and immune-mediated diseases resulting from dysregulation of the immune response after exposure to agents with adjuvant activity. This case report describes the development of large artery vasculitis, TA, in an individual one year following the placement of silicone breast implants. The patient initially presented with non-specific symptoms, and multiple imaging methods were employed, including ultrasound diagnostics, CT angiography, and 18-fluorodeoxyglucose positron emission tomography/CT. These techniques revealed vasculitic alterations in the carotid arteries and thoracic aorta. Initial treatment with glucocorticosteroids proved ineffective, prompting the addition of steroid-sparing immunosuppressive agents. Due to the distinct clinical symptoms, disease progression, implant-associated fibrosis, and resistance to therapy, the potential involvement of implants in the development of large-vessel vasculitis was considered, and a potential association with ASIA was postulated. Although there is limited evidence to support a direct link between adjuvants and the pathogenesis of TA, similarities in cellular immunity between the two conditions exist. The diagnosis of this complex and potentially debilitating condition requires a comprehensive clinical examination, laboratory evaluation, and instrumental assessment. This will aid in identifying potential contributing factors and ensuring successful treatment.
Takayasu 动脉炎(TA)是一种主要影响主动脉及其主要分支的慢性肉芽肿性血管炎。尽管人们对血管炎症的发病机制途径有了更多的了解,但 TA 的病因和易患因素仍未完全了解。在易感个体中,接触佐剂可能会引发、解锁或揭示自身免疫性疾病,表现为非特异性全身症状或完全发展的自身免疫综合征,如血管炎。在这里,我们假设 TA 可能是由硅肺引起的,硅肺是佐剂引起的自身免疫/炎症综合征(ASIA)的一个亚型。ASIA 也称为 Shoenfeld 综合征,包括一系列自身免疫和免疫介导的疾病,这些疾病是由于接触具有佐剂活性的药物后免疫反应失调而引起的。本病例报告描述了一名个体在放置硅酮乳房植入物一年后发生大动脉血管炎 TA。患者最初表现为非特异性症状,并采用了多种影像学方法,包括超声诊断、CT 血管造影和 18-氟脱氧葡萄糖正电子发射断层扫描/CT。这些技术显示颈动脉和胸主动脉存在血管炎改变。最初使用糖皮质激素治疗无效,随后加入了类固醇保肺免疫抑制剂。由于独特的临床症状、疾病进展、植入物相关纤维化和对治疗的抵抗,考虑到植入物可能参与大血管血管炎的发生,并推测与 ASIA 有关。尽管有有限的证据支持佐剂与 TA 发病机制之间存在直接联系,但两种情况下的细胞免疫存在相似之处。这种复杂且潜在致残疾病的诊断需要全面的临床检查、实验室评估和仪器评估。这将有助于确定潜在的促成因素并确保成功治疗。