Intraperitoneal rhabdoid tumor with spontaneous internal bleeding in a 9-year-old child: A rare case report.

INTRODUCTION AND IMPORTANCE

Malignant rhabdoid tumor is a rare malignancy which occurs in children with limited cases reported.

CASE PRESENTATION

We report a very rare primary intraperitoneal rhabdoid tumor in a 9-year-old female child. The only case was first reported in a 10-year old girl in 2014 (Nam et al., 2014 [1]). The diagnostic became a problem as the case was initially diagnosed as Ovarian Malignancy. It did not match the initial abdominal Computed Tomography (CT) imaging which showed a bilateral malignant ovarian tumor that resembled Ovarian Carcinoma.

CLINICAL DISCUSSION

Preoperative diagnosis of intraperitoneal Rhabdoid tumor is difficult, as it commonly occurs in the brain (ATRT) or Kidney (MRTK) and rarely occurs intraperitoneally. Moreover, the clinical symptom and radiologic findings in this tumor remained unclear. Most cases had CT Scan findings as heterogenous enhancing nodules with central necrosis (hypodense) and usually metastatic. The definitive diagnosis of Rhabdoid Tumor is based on post-resection histopathology and immunohistochemistry (IHC).

CONCLUSION

The intraperitoneal rhabdoid tumor is rare and has an extremely poor prognosis. The physicians should be alert when finding intraabdominal mass; rhabdoid tumor should be the differential diagnosis.