10岁女孩大网膜原发性恶性横纹肌样瘤

Primary malignant rhabdoid tumor of greater omentum in 10-year-old girl.

作者信息

Nam So-Hyun, Park Jeong-A, Kim Yeon Mee

机构信息

Department of Pediatric Surgery, Inje University Haeundae Paik Hospital, Busan, Korea.

Department of Pediatrics, Inje University Haeundae Paik Hospital, Busan, Korea.

出版信息

Ann Surg Treat Res. 2014 Jan;86(1):50-3. doi: 10.4174/astr.2014.86.1.50. Epub 2014 Jan 1.

DOI:10.4174/astr.2014.86.1.50

PMID:24761408

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3994608/

Abstract

Contrary to metastatic tumors of the omentum, primary tumors of the omentum are very rare. A 10-year-old girl presented with low abdominal pain. Imaging studies showed a multiseptated hemorrhagic tumor. The mass from the omentum was removed completely and confirmed as a malignant rhabdoid tumor. Despite aggressive chemotherapy, she died after 9 months due to disease progression. We report one case of primary malignant rhabdoid tumor of the omentum for the first time.

摘要

与大网膜转移性肿瘤相反，原发性大网膜肿瘤非常罕见。一名10岁女孩出现下腹部疼痛。影像学检查显示为多房性出血性肿瘤。完整切除了来自大网膜的肿物，确诊为恶性横纹肌样瘤。尽管进行了积极的化疗，但她在9个月后因疾病进展而死亡。我们首次报告一例原发性大网膜恶性横纹肌样瘤病例。