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[原发性纵隔B细胞淋巴瘤孕妇的心血管并发症]

[Cardiovascular complications in pregnant woman with Primary Mediastinal B-Cell Lymphoma].

作者信息

Inquilla Coyla Melisa, Anchante Hernández Henry, Medina Palomino Félix

机构信息

Hospital Cayetano Heredia, Lima - Perú. Hospital Cayetano Heredia Lima Perú.

出版信息

Arch Peru Cardiol Cir Cardiovasc. 2022 Jun 27;3(2):112-116. doi: 10.47487/apcyccv.v3i2.202. eCollection 2022 Apr-Jun.

DOI:10.47487/apcyccv.v3i2.202
PMID:37283601
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10241342/
Abstract

A 26-year-old pregnant woman with 29 weeks of gestational age reported two months of cough, dyspnea, orthopnea, and palpitations. Chest tomography revealed a 10x12cm solid mass in the right lung. Echocardiography showed that the tumor compromised the right atrium and ventricle, and was diagnosed by transcutaneous biopsy as Primary Mediastinal B-Cell Lymphoma (PMCBL). The patient presented 2:1 atrial flutter, sinus bradycardia, and ectopic atrial bradycardia. Due to the rapid poor evolution, it was decided to terminate the pregnancy by cesarean section and start chemotherapy, after which the cardiovascular complications resolved. PCML is a very rare lymphoma that can affect pregnant women in any trimester, its symptoms are related to its rapid growth and compromise of the heart, causing various cardiovascular manifestations (heart failure, pericardial effusion, cardiac arrhythmias). PCMLC is characteristically chemosensitive and has a good prognosis.

摘要

一名孕29周的26岁孕妇报告有两个月的咳嗽、呼吸困难、端坐呼吸和心悸症状。胸部断层扫描显示右肺有一个10×12厘米的实性肿块。超声心动图显示肿瘤累及右心房和右心室,经皮活检诊断为原发性纵隔B细胞淋巴瘤(PMCBL)。该患者出现2:1心房扑动、窦性心动过缓和异位房性心动过缓。由于病情迅速恶化,决定通过剖宫产终止妊娠并开始化疗,化疗后心血管并发症得以缓解。原发性纵隔B细胞淋巴瘤是一种非常罕见的淋巴瘤,可在任何孕期影响孕妇,其症状与其快速生长和心脏受累有关,可导致各种心血管表现(心力衰竭、心包积液、心律失常)。原发性纵隔B细胞淋巴瘤对化疗具有特征性敏感性,预后良好。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/5c7926a9e8fa/apcyccv-3-112-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/4a996bb1e78a/apcyccv-3-112-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/3e6deebc5b6d/apcyccv-3-112-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/f144f6664f78/apcyccv-3-112-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/781c93866d9e/apcyccv-3-112-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/5c7926a9e8fa/apcyccv-3-112-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/4a996bb1e78a/apcyccv-3-112-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/3e6deebc5b6d/apcyccv-3-112-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/f144f6664f78/apcyccv-3-112-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/781c93866d9e/apcyccv-3-112-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a889/10241342/5c7926a9e8fa/apcyccv-3-112-g005.jpg

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JACC CardioOncol. 2020 Jun 16;2(2):293-311. doi: 10.1016/j.jaccao.2020.05.009. eCollection 2020 Jun.
2
Infiltrative Lymphoma-Associated Bradycardia and Cardiac Conduction Abnormalities.浸润性淋巴瘤相关的心动过缓和心脏传导异常。
JACC CardioOncol. 2020 Mar 17;2(1):135-138. doi: 10.1016/j.jaccao.2020.01.002. eCollection 2020 Mar.
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Cardiac Involvement by Burkitt Lymphoma in a 49-Year-Old Man.一名49岁男性患者的伯基特淋巴瘤累及心脏
Tex Heart Inst J. 2020 Jun 1;47(3):210-212. doi: 10.14503/THIJ-17-6448.
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Cardiac Tumors: Clinical Presentation, Diagnosis, and Management.心脏肿瘤:临床特征、诊断与处理。
Curr Treat Options Oncol. 2019 Jun 27;20(8):66. doi: 10.1007/s11864-019-0662-1.
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The unique biology and treatment of primary mediastinal B-cell lymphoma.原发性纵隔B细胞淋巴瘤的独特生物学特性与治疗方法
Best Pract Res Clin Haematol. 2018 Sep;31(3):241-250. doi: 10.1016/j.beha.2018.07.001. Epub 2018 Jul 3.
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Superior vena cava syndrome related to mediastinal lymphoma in late pregnancy: A case report.
Case Rep Womens Health. 2018 May 26;19:e00065. doi: 10.1016/j.crwh.2018.e00065. eCollection 2018 Jul.
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Primary mediastinal large B-cell lymphoma.原发性纵隔大B细胞淋巴瘤
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Primary mediastinal large B-cell lymphoma in pregnancy.妊娠期原发性纵隔大B细胞淋巴瘤
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[Primary mediastinal large B-cell lymphoma in pregnant women].[孕妇原发性纵隔大B细胞淋巴瘤]
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