Kayedi Mehrdad, Kian Behnam, Teimouri Arash
Medical Imaging Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
Medical Imaging Research Center, Zahedan University of Medical Sciences, Zahedan, Iran.
Radiol Case Rep. 2022 Jul 28;17(10):3551-3555. doi: 10.1016/j.radcr.2022.06.093. eCollection 2022 Oct.
Abernethy malformation or congenital portosystemic shunt is a rare congenital vascular malformation and anomaly of the splanchnic venous system defined by diverting portal blood away from the liver. It is commonly associated with multiple congenital anomalies. Imaging modalities such as computed tomography or magnetic resonance have a crucial role in prompting diagnosis and determining the prognosis based on the type of malformation and associated anomalies. Misdiagnosis could be harmful and may lead to inappropriate treatment. We present a case of Abernethy malformation with a complete end-to-side shunt of portal venous flow into the systemic venous flow and complete bypass of the liver, which was initially misdiagnosed with portal venous thrombosis.
阿伯内西畸形或先天性门体分流是一种罕见的先天性血管畸形，是内脏静脉系统的异常，其定义为门静脉血从肝脏分流。它通常与多种先天性异常相关。计算机断层扫描或磁共振成像等影像学检查在基于畸形类型和相关异常进行诊断提示及判断预后方面起着关键作用。误诊可能有害，可能导致不适当的治疗。我们报告一例阿伯内西畸形病例，门静脉血流完全端侧分流至体循环静脉血流，肝脏完全被绕过，该病例最初被误诊为门静脉血栓形成。
