Ohar J M, Robichaud A M, Fowler A A, Glauser F L
Am J Med. 1986 Aug;81(2):361-2. doi: 10.1016/0002-9343(86)90280-9.
Pulmonary artery vasospasm is a hypothesized antecedent and etiologic factor in the pulmonary hypertension associated with progressive systemic sclerosis. Recent clinical data refute the existence of pulmonary vasospasm in a cohort of patients with scleroderma and normal baseline pulmonary artery pressure. A case of episodic pulmonary hypertension associated with a digital Raynaud's response is reported, and a cardiac mechanism is hypothesized.
肺动脉血管痉挛被认为是进行性系统性硬化症相关肺动脉高压的一个假定的前期和病因学因素。最近的临床数据驳斥了硬皮病且基线肺动脉压正常的一组患者中存在肺动脉血管痉挛的观点。本文报告了一例与指端雷诺反应相关的发作性肺动脉高压病例，并推测其存在心脏机制。
