Chauhan Bhanu Pratap Singh, Dholakia Binita, Singh Daljit
Department of Neurosurgery, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research, New Delhi, India.
Surg Neurol Int. 2023 Jun 23;14:215. doi: 10.25259/SNI_341_2023. eCollection 2023.
Encephalocele is herniation of cranial contents through a skull defect, classified according to their contents and location, and is usually seen in pediatric age group. The transsphenoidal type represents <5% of all basal meningoencephaloceles. Of them, the presentation in adulthood is even rarer.
A 19-year-old female complaining of breathing difficulties during sleep and exertional dyspnea was diagnosed with a transsphenoidal meningoencephalocele, likely representing patent craniopharyngeal canal. On exploration through bifrontal craniotomy, the defect was identified in the sellar floor after completely reducing the contents into the cranial cavity and was repaired. She had immediate symptomatic relief and an uneventful postoperative course.
There can be significant symptomatic relief with minimal postoperative morbidity after transcranial repair of such large transsphenoidal meningoencephaloceles, through traditional skull base approaches.
脑膨出是指颅骨内容物通过颅骨缺损处疝出，根据其内容物和位置进行分类，常见于儿童年龄组。经蝶型脑膨出占所有基底脑膜脑膨出的比例不到5%。其中，成年期发病更为罕见。
一名19岁女性，主诉睡眠时呼吸困难和劳力性呼吸困难，被诊断为经蝶型脑膜脑膨出，可能是颅咽管未闭。通过双额开颅手术进行探查，在将内容物完全还纳至颅腔后，在蝶鞍底部发现缺损并进行了修复。她术后症状立即缓解，术后过程顺利。
通过传统的颅底入路，经颅修复此类大型经蝶型脑膜脑膨出，术后发病率极低，可显著缓解症状。
