Bigdelu Leila, Maadarani Ossama, Azari Ali, Heidari-Bakavoli Ali, Bitar Zouheir
Cardiovascular Medicine Division, Vascular Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran.
Critical Care Unit, Internal Medical Department, Ahmadi Hospital (KOC), Kuwait.
Eur J Case Rep Intern Med. 2023 Jun 26;10(7):003962. doi: 10.12890/2023_003962. eCollection 2023.
Anomalous left coronary artery from the pulmonary artery (ALCAPA) is considered a rare congenital heart disease where the take-off of the left coronary artery abnormally originates from the pulmonary artery instead of left aortic sinus. It is associated with a high mortality rate in the first year of life and sudden death in adults if left untreated. We report an adult form of ALCAPA syndrome in a 20-year-old female who presented with anginal pain for the previous few months. Unfortunately, the patient was hesitant to have surgery at the time.
The abnormal origin of the left coronary artery from the pulmonary artery (ALCAPA) is rare and potentially fatal coronary congenital disease, accounting for 0.5% of all congenital heart diseases; it is associated with poor outcomes if left untreated.ALCAPA is classified into infantile and adult forms. The prevalence of adult individuals with ALCAPA syndrome has significantly increased as a result of recent developments in non-invasive cardiac imaging.The prevalence of sudden mortality in childhood and the early stages of adulthood makes surgery the preferred treatment, and coronary reimplantation surgery is considered the surgical procedure of choice.
起源于肺动脉的异常左冠状动脉（ALCAPA）被认为是一种罕见的先天性心脏病，即左冠状动脉的起始异常地源自肺动脉而非左主动脉窦。如果不进行治疗，它在生命的第一年具有较高的死亡率，在成年人中则会导致猝死。我们报告了一名20岁女性的成人型ALCAPA综合征病例，该患者在过去几个月中出现了心绞痛症状。不幸的是，该患者当时对手术犹豫不决。
起源于肺动脉的异常左冠状动脉（ALCAPA）是一种罕见且潜在致命的冠状动脉先天性疾病，占所有先天性心脏病的0.5%；如果不进行治疗，其预后较差。ALCAPA分为婴儿型和成人型。由于无创心脏成像技术的最新发展，患有ALCAPA综合征的成年个体的患病率显著增加。儿童期和成年早期的猝死患病率使得手术成为首选治疗方法，冠状动脉再植手术被认为是首选的手术方式。
