Lack E E, Dolan M F, Finisio J, Grover G, Singh M, Triche T J
Am J Surg Pathol. 1986 Sep;10(9):650-7. doi: 10.1097/00000478-198609000-00007.
The authors report an extraordinary case of a 33-year-old female who had pulmonary and extrapulmonary lymphangioleiomyomatosis, bilateral renal angiomyolipomas, multifocal lymphangioleiomyomatosis involving the uterus, ovaries, periadrenal vessels, and liver. The patient also had a glial polyp of the endocervix which represented retained fetal parts from an abortion 15 years earlier. Both ovaries showed multiple follicle cysts which may have been a source of endogenous estrogen. The classical stigmata of the tuberous sclerosis complex were absent. The multifocal lymphangioleiomyomatosis of the various organs described presents an extremely rare manifestation of this disorder.
作者报告了一例罕见病例，一名33岁女性患有肺和肺外淋巴管平滑肌瘤病、双侧肾血管平滑肌脂肪瘤、多灶性淋巴管平滑肌瘤病累及子宫、卵巢、肾上腺周围血管和肝脏。该患者还患有宫颈神经胶质息肉，这是15年前一次流产后残留的胎儿组织。双侧卵巢均显示多个卵泡囊肿，这可能是内源性雌激素的来源。该患者没有结节性硬化症的典型体征。所描述的各个器官的多灶性淋巴管平滑肌瘤病是这种疾病极为罕见的表现形式。
