Orlando Porras Bueno Cristian, Ines Saldarriaga Giraldo Clara, Eduardo Roncancio Villamil Gustavo, Fernanda Álvarez Barreneche María
Department of Internal Medicine Autonomous University of Bucaramanga Bucaramanga Colombia.
Department of Cardiology and Heart Failure Universidad de Antioquía, Universidad Pontificia Bolivariana, Clínica Cardio VID Medellín Colombia.
Clin Case Rep. 2023 Aug 2;11(8):e7749. doi: 10.1002/ccr3.7749. eCollection 2023 Aug.
Heart failure due to ANCA-negative vasculitis, is a rare potentially life-threatening manifestation of ANCA vasculitis. Therefore, physicians must always pay attention to this manifestation for proper disease diagnosis and treatment.
Less than 10% of primary vasculitides cause cardiac dysfunction, with Takayasu's arteritis, polyarteritis nodosa, and eosinophilic granulomatosis with polyangiitis being the most common cases. However, any cardiac tissue can be affected by ANCA vasculitis. We present a case of heart failure with reduced ventricular ejection fraction due to ANCA negative-vasculitis.
抗中性粒细胞胞浆抗体(ANCA)阴性血管炎所致心力衰竭是ANCA血管炎一种罕见但可能危及生命的表现形式。因此,医生必须始终关注这一表现,以便进行正确的疾病诊断和治疗。
不到10%的原发性血管炎会导致心脏功能障碍,其中最常见的病例是大动脉炎、结节性多动脉炎和嗜酸性肉芽肿性多血管炎。然而,任何心脏组织都可能受到ANCA血管炎的影响。我们报告一例因ANCA阴性血管炎导致心室射血分数降低的心力衰竭病例。