Ramdani Mohammed, El Moudane Anouar, Tahri Youness, Jdaini Ahmed, Benamou Achraf, Mokhtari Mohamed, Barki Ali
Urology, Mohammed VI University Hospital Oujda, Oujda, MAR.
Urology, Faculty of Medicine and Pharmacy of Oujda, Oujda, MAR.
Cureus. 2023 Aug 1;15(8):e42797. doi: 10.7759/cureus.42797. eCollection 2023 Aug.
The association between Klippel-Trenauney syndrome (KTS) and bladder hemangiomas is rare. The most common clinical manifestation is hematuria. The diagnosis is made from the characteristic cystoscopic appearance of the tumor. We report the case of a patient presenting recurrent macroscopic hematuria in the context of KTS. A cystoscopic evaluation revealed bladder hemangiomas. A conservative approach consisting of bladder irrigation and close follow-up was chosen as therapy. Conservative treatment of bladder irrigation and close follow-up is the recommended initial treatment of moderate and infrequent episodes of hematuria in this context. The more invasive therapeutic options have to be considered especially for frequent or life-threatening episodes of hematuria. This case suggests that conservative treatment may be effective in treating moderate and infrequent episodes of hematuria due to bladder hemangioma in the context of KTS. Further studies are required to adequately establish the effectiveness, limitations, and complications of each approach.
克-特综合征（KTS）与膀胱血管瘤之间的关联较为罕见。最常见的临床表现是血尿。诊断依据肿瘤特征性的膀胱镜表现做出。我们报告一例在KTS背景下出现反复肉眼血尿的患者。膀胱镜检查发现膀胱血管瘤。选择膀胱冲洗及密切随访的保守方法作为治疗手段。在这种情况下，膀胱冲洗及密切随访的保守治疗是推荐用于治疗中度且不频繁血尿发作的初始治疗方法。对于频繁或危及生命的血尿发作，尤其必须考虑更具侵入性的治疗选择。该病例提示，在KTS背景下，保守治疗对于因膀胱血管瘤导致的中度且不频繁血尿发作可能有效。需要进一步研究以充分确定每种治疗方法的有效性、局限性及并发症。
