Shah Dharmendra, Chaudhary Shivani R, Khan Shahin, Mallik Shashwat
General Surgery, Medical College Baroda, Vadodara, IND.
Cureus. 2023 Aug 22;15(8):e43914. doi: 10.7759/cureus.43914. eCollection 2023 Aug.
Ganglioneuroma is a rare, benign, well-differentiated neurogenic tumor most commonly located in the posterior mediastinum or retroperitoneum. Giant ganglioneuromas are even less common; this is only the 19th reported case in literature to date. We present a case of a giant retroperitoneal ganglioneuroma in a five-year-old child, which on imaging mimicked a mesenteric cyst and posed various challenges in its management. Histopathology later confirmed our misdiagnosis and revealed the tumor to be a ganglioneuroma. This unique case serves as a lesson for clinicians to not operate before receiving histopathological confirmation of their diagnosis.
神经节神经瘤是一种罕见的、良性的、分化良好的神经源性肿瘤，最常见于后纵隔或腹膜后。巨大神经节神经瘤更为罕见；这是迄今为止文献报道的第19例。我们报告一例5岁儿童的巨大腹膜后神经节神经瘤，其影像学表现酷似肠系膜囊肿，在治疗上带来了各种挑战。组织病理学后来证实了我们的误诊，显示该肿瘤为神经节神经瘤。这个独特的病例给临床医生上了一课，即在未获得诊断的组织病理学确认之前不要进行手术。
