Department of Pediatrics, Division of Pediatric Gastroenterology, Hepatology and Nutrition, Cardinal Glennon Children's Medical Center, Saint Louis University School of Medicine, St. Louis, MO 63104, USA.
The AHEAD Institute, Saint Louis University School of Medicine, St. Louis, MO 63104, USA.
Int J Mol Sci. 2023 Oct 30;24(21):15766. doi: 10.3390/ijms242115766.
Cystic Fibrosis is a chronic disease affecting multiple systems, including the GI tract. Clinical manifestation in patients can start as early as infancy and vary across different age groups. With the advent of new, highly effective modulators, the life expectancy of PwCF has improved significantly. Various GI aspects of CF care, such as nutrition, are linked to an overall improvement in morbidity, lung function and the quality of life of PwCF. The variable clinical presentations and management of GI diseases in pediatrics and adults with CF should be recognized. Therefore, it is necessary to ensure efficient transfer of information between pediatric and adult providers for proper continuity of management and coordination of care at the time of transition. The transition of care is a challenging process for both patients and providers and currently there are no specific tools for GI providers to help ensure a smooth transition. In this review, we aim to highlight the crucial features of GI care at the time of transition and provide a checklist that can assist in ensuring an effective transition and ease the challenges associated with it.
囊性纤维化是一种影响多个系统的慢性疾病，包括胃肠道。患者的临床表现最早可在婴儿期出现，并在不同年龄组中有所不同。随着新型、高效调节剂的出现，囊性纤维化患者的预期寿命显著提高。囊性纤维化患者的各种胃肠道方面的护理，如营养，与发病率、肺功能和生活质量的整体改善有关。儿科和成人囊性纤维化患者的胃肠道疾病的临床表现和管理各不相同，因此，有必要确保儿科和成人提供者之间的信息高效传递，以便在过渡时对管理进行适当的连续性和护理协调。护理的过渡对患者和提供者来说都是一个具有挑战性的过程，目前还没有专门针对胃肠道提供者的工具来帮助确保平稳过渡。在这篇综述中，我们旨在强调过渡时胃肠道护理的关键特征，并提供一个检查表，以帮助确保有效的过渡，并减轻与之相关的挑战。
