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一例伴有色素性视网膜炎的色素性静脉旁视网膜脉络膜萎缩病例。

A Case of Pigmented Paravenous Retinochoroidal Atrophy With Retinitis Pigmentosa.

作者信息

Fukushima Atsuki, Tabuchi Hitoshi

机构信息

Ophthalmology, Tsukazaki Hospital, Himeji, JPN.

Ophthalmology, Hiroshima University, Hiroshima, JPN.

出版信息

Cureus. 2023 Nov 8;15(11):e48532. doi: 10.7759/cureus.48532. eCollection 2023 Nov.

DOI:10.7759/cureus.48532
PMID:38074014
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10709112/
Abstract

Chorioretinal atrophy with pigmentation along the retinal veins was observed in the right fundus of a 49-year-old patient. Extensive retinitis pigmentosa (RP) was observed in the left eye. Dynamic quantitative visual field testing revealed a scotoma in the right eye that corresponded to the area of ​​retinochoroidal atrophy and afferent visual field constriction was observed on the left eye. An electroretinogram test revealed that the right eye showed attenuated type and the left eye showed negative type. Thus, the conditions of his right eye and left eye were diagnosed as pigmented paravenous retinochoroidal atrophy (PPRCA) and RP, respectively. Thus, there may be a higher proportion of PPRCA patients with unilateral RP than expected.

摘要

在一名49岁患者的右眼眼底观察到沿视网膜静脉的脉络膜视网膜萎缩伴色素沉着。左眼观察到广泛的视网膜色素变性（RP）。动态定量视野测试显示右眼有一个与视网膜脉络膜萎缩区域相对应的暗点，左眼观察到传入性视野缩窄。视网膜电图测试显示右眼为衰减型，左眼为阴性型。因此，他的右眼和左眼情况分别被诊断为色素性静脉旁视网膜脉络膜萎缩（PPRCA）和RP。因此，单侧RP的PPRCA患者比例可能比预期的更高。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/5a019ef29783/cureus-0015-00000048532-i07.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/182240e9c4cc/cureus-0015-00000048532-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/8d154d2d981b/cureus-0015-00000048532-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/adad5898b25b/cureus-0015-00000048532-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/6718a253f942/cureus-0015-00000048532-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/487c44a579c0/cureus-0015-00000048532-i05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/7e396eecc024/cureus-0015-00000048532-i06.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/5a019ef29783/cureus-0015-00000048532-i07.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/182240e9c4cc/cureus-0015-00000048532-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/8d154d2d981b/cureus-0015-00000048532-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/adad5898b25b/cureus-0015-00000048532-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/6718a253f942/cureus-0015-00000048532-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/487c44a579c0/cureus-0015-00000048532-i05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/7e396eecc024/cureus-0015-00000048532-i06.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2fb9/10709112/5a019ef29783/cureus-0015-00000048532-i07.jpg

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本文引用的文献

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Eur J Ophthalmol. 2024 Jul;34(4):941-951. doi: 10.1177/11206721231199118. Epub 2023 Sep 5.
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variant associated with pigmented paravenous chorioretinal atrophy.与色素性静脉旁脉络膜视网膜萎缩相关的变体
Eur J Ophthalmol. 2023 Nov;33(6):NP6-NP9. doi: 10.1177/11206721231155042. Epub 2023 Feb 8.
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Pigmented paravenous retinochoroidal atrophy associated with Vogt-Koyanagi-Harada disease: a case report.色素性静脉旁视网膜脉络膜萎缩与 Vogt-Koyanagi-Harada 病相关：一例报告。
BMC Ophthalmol. 2020 Jan 29;20(1):36. doi: 10.1186/s12886-020-1318-4.
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Rare case of simultaneous manifestation of pigmented paravenous retinochoroidal atrophy and retinitis pigmentosa in contralateral eye.色素性静脉旁视网膜脉络膜萎缩与色素性视网膜炎同时累及对侧眼的罕见病例。
Indian J Ophthalmol. 2019 Nov;67(11):1875-1876. doi: 10.4103/ijo.IJO_372_19.
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Ultra-wide field imaging of pigmented para-venous retino-choroidal atrophy.色素性静脉旁视网膜脉络膜萎缩的超广角成像
Eur J Ophthalmol. 2019 Jul;29(4):444-452. doi: 10.1177/1120672118795056. Epub 2018 Sep 3.
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