Vital A, Vital C, Guerin J, Leman P, Geniaux M, Mouton L, Texier L
Ann Pathol. 1985;5(4-5):327-9.
The central nervous system may be involved in Degos disease, but neuropathologic observations are still few. We report a typical case with cerebral involvement. The diagnosis was suggested by the characteristic skin lesions and vascular damage. In the central nervous system, occlusive changes of small arteries were responsible for areas of ischaemic necrosis. These foci of infarction were of varying size, age and distribution. Intestinal lesions were discrete and death was due to several cerebral infarcts.
中枢神经系统可能会累及德戈斯病,但神经病理学观察仍然较少。我们报告一例典型的脑部受累病例。特征性皮肤病变和血管损伤提示了诊断。在中枢神经系统中,小动脉的闭塞性改变导致了缺血性坏死区域。这些梗死灶大小、时期和分布各异。肠道病变是散在的,死亡原因是多处脑梗死。