Department of Pediatric Pulmonology, Ankara Bilkent City Hospital, Ankara, Turkey.
Department of Pediatric Pulmonology, School of Medicine, Hacettepe University, Ihsan Dogramaci Children's Hospital, Ankara, Turkey.
Eur J Pediatr. 2024 May;183(5):2333-2342. doi: 10.1007/s00431-024-05479-6. Epub 2024 Mar 2.
Cystic fibrosis (CF) is a multisystemic disease in which airway obstruction, infection, and inflammation play a critical role in the pathogenesis and progression of CF lung disease. The carbohydrate-binding protein Galectin-3 is increased in several inflammatory and fibrotic diseases and has recently been forwarded as a biomarker in these diseases. We aimed to define the role of serum Galectin-3 in children with CF by comparison with healthy subjects. This is a cross-sectional, case-control study. 143 CF and 30 healthy subjects were enrolled in the study. Peripheral blood and sputum concentrations of Galectins-3, interleukin (IL)-17A, IL-8, and neutrophil elastase (NE) were determined with commercial ELISA kits. There was no significant difference between the groups in age and gender (p = 0.592, p = 0.613, respectively). Serum Galectin-3 and NE concentrations were higher in the patient group than in healthy controls (p = 0.002, p < 0.001, respectively). There were no significant differences between groups according to IL-17A and IL-8 concentrations. Serum Galectin-3 was correlated with age (r = 0.289, p < 0.001) and body mass index (BMI) (r = 0.493, p < 0.001) in children with CF. Sputum Galectin-3 levels are negatively correlated with percent predictive forced expiratory volume in 1 s (FEV1) (r = - 0.297, p = 0.029), FEV1 z-score, (r = - 0.316, p = 0.020), percent predictive forced vital capacity (FVC) (r = - 0.347, p = 0.010), and FVC z-score (r = - 0.373, p = 0.006). Conclusion: The study shows that serum Galectin-3 levels increased in clinically stable CF patients, and serum Galectin-3 response may depend on age, gender, and BMI. The sputum Galectin-3 was found to be negatively correlated with patients' lung functions. What is known: • Galectin-3 is a key regulator of chronic inflammation in the lung, liver, kidney, and tumor microenvironment. What is new: • Children with cystic fibrosis (CF) have higher serum Galectin-3 concentrations than healthy children. • Serum Galectin-3 expression influenced by age, BMI, and gender in children with CF.
囊性纤维化(CF)是一种多系统疾病,气道阻塞、感染和炎症在 CF 肺部疾病的发病机制和进展中起着关键作用。糖结合蛋白半乳糖凝集素-3 在几种炎症性和纤维化疾病中增加,并最近被提出作为这些疾病的生物标志物。我们旨在通过与健康受试者进行比较来确定血清半乳糖凝集素-3在 CF 儿童中的作用。这是一项横断面病例对照研究。研究纳入了 143 名 CF 患者和 30 名健康受试者。使用商业 ELISA 试剂盒测定外周血和痰中半乳糖凝集素-3、白细胞介素(IL)-17A、IL-8 和中性粒细胞弹性蛋白酶(NE)的浓度。两组在年龄和性别方面无显著差异(p=0.592,p=0.613)。与健康对照组相比,患者组的血清半乳糖凝集素-3和 NE 浓度更高(p=0.002,p<0.001)。两组间 IL-17A 和 IL-8 浓度无显著差异。在 CF 患儿中,血清半乳糖凝集素-3与年龄(r=0.289,p<0.001)和体重指数(BMI)(r=0.493,p<0.001)相关。痰半乳糖凝集素-3水平与 1 秒用力呼气量预测值(FEV1)(r= -0.297,p=0.029)、FEV1 z 评分(r= -0.316,p=0.020)、用力肺活量预测值(FVC)(r= -0.347,p=0.010)和 FVC z 评分(r= -0.373,p=0.006)呈负相关。结论:本研究表明,临床稳定的 CF 患者血清半乳糖凝集素-3 水平升高,血清半乳糖凝集素-3 反应可能取决于年龄、性别和 BMI。痰半乳糖凝集素-3 与患者的肺功能呈负相关。已知内容:• 半乳糖凝集素-3 是肺部、肝脏、肾脏和肿瘤微环境中慢性炎症的关键调节剂。新内容:• 囊性纤维化(CF)患儿的血清半乳糖凝集素-3 浓度高于健康儿童。• CF 患儿的血清半乳糖凝集素-3 表达受年龄、BMI 和性别影响。