Haghgoo Ameneh, Faegh Ali, Nasiri Saeed, Akhbari Farnaz
School of Medicine Iran University of Medical Sciences Tehran Iran.
School of Medicine Alborz University of Medical Sciences Karaj Iran.
Clin Case Rep. 2024 Mar 14;12(3):e8661. doi: 10.1002/ccr3.8661. eCollection 2024 Mar.
OHVIRA syndrome can be misdiagnosed due to its rarity, resulting in the need for more invasive interventions than vaginoscopy. Also, delayed diagnosis of OHVIRA syndrome can affect patient's quality of life by leading to chronic gynecological diseases such as endometriosis and pelvic inflammatory disease.
Obstructive hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome is one of the infrequent congenital Mullerian duct anomalies characterized by obstructed hemivagina and ipsilateral renal agenesis. This study presents a 20-year-old virgin female who was diagnosed with OHVIRA syndrome and treated by vaginoscopy using the hymen preservation technique. Also, she was misdiagnosed with non-communicating rudimentary uterine horn 4 years ago. Late or misdiagnosis of OHVIRA syndrome can affect fertility and pregnancy outcomes. Therefore, early diagnosis and management are crucial. OHVIRA syndrome's misdiagnosis is possible with other Mullerian duct anomalies, such as a rudimentary uterine horn. Also, patients with misdiagnosis undergo unnecessary interventions.
OHVIRA综合征因其罕见性可能被误诊，从而导致比阴道镜检查更具侵入性的干预需求。此外，OHVIRA综合征的延迟诊断会导致子宫内膜异位症和盆腔炎等慢性妇科疾病，进而影响患者的生活质量。
梗阻性半阴道并同侧肾缺如（OHVIRA）综合征是一种罕见的先天性苗勒管异常，其特征为半阴道梗阻和同侧肾缺如。本研究报告了一名20岁的未婚女性，她被诊断为OHVIRA综合征，并采用保留处女膜技术经阴道镜进行治疗。此外，她在4年前曾被误诊为非交通性残角子宫。OHVIRA综合征的延迟或误诊会影响生育能力和妊娠结局。因此，早期诊断和治疗至关重要。OHVIRA综合征有可能与其他苗勒管异常，如残角子宫相混淆。此外，误诊的患者会接受不必要的干预。
