一名成年Silver-Russell综合征患者的麻醉经历：病例报告
Anesthesia experience in an adult Silver-Russell syndrome: a case report.
作者信息
Hibino Akinobu, Hibino Ayaka, Kamiya Yoshinori
机构信息
Department of Anesthesiology, Shibata Hospital Niigata Prefectural Hospital, 1-2-8 Honcho, Shibata City, Niigata 957-8588, Japan.
Department of Anesthesiology, Niigata University Medical and Dental Hospital, 1-754 Asahimachi-Dori, Chuo-Ku, Niigata City, Niigata 951-8510, Japan.
出版信息
JA Clin Rep. 2024 Apr 3;10(1):20. doi: 10.1186/s40981-024-00704-5.
BACKGROUND
There are no reports of anesthesia use in adult patients with Silver-Russell syndrome (SRS). Here, we report our experience with anesthesia in an adult patient with SRS complicated by chronic respiratory failure.
CASE PRESENTATION
A 33-year-old woman was clinically diagnosed with SRS. She had severe chronic respiratory failure, complicated by superior mesenteric artery syndrome. Percutaneous gastrostomy was scheduled for nutritional management under epidural anesthesia; however, soon after esophagogastroduodenoscopy was started, she lost consciousness and spontaneous respiration. The patient was urgently intubated and converted to general anesthesia. The end-tidal carbon dioxide tension was > 90 mmHg at intubation.
CONCLUSIONS
Adult SRS patients with chronic respiratory failure have a risk of CO narcosis. SRS also requires preparation for difficult airway management during the perioperative period.
背景
尚无关于成人Silver-Russell综合征（SRS）患者麻醉使用情况的报道。在此，我们报告1例合并慢性呼吸衰竭的成年SRS患者的麻醉经验。
病例介绍
一名33岁女性经临床诊断为SRS。她患有严重的慢性呼吸衰竭，并伴有肠系膜上动脉综合征。计划在硬膜外麻醉下进行经皮胃造口术以进行营养管理；然而，在开始食管胃十二指肠镜检查后不久，她失去意识并停止自主呼吸。患者紧急插管并转为全身麻醉。插管时呼气末二氧化碳分压>90 mmHg。
结论
合并慢性呼吸衰竭的成年SRS患者有发生CO麻醉的风险。SRS在围手术期也需要做好困难气道管理的准备。
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