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梅杰综合征患者难治性眼睑痉挛的手术性肌切除术和肌切开术:一例报告

Surgical Myectomy and Myotomy for Refractory Blepharospasm in Meige Syndrome Patients: A Case Report.

作者信息

Li Ming-Ming, Cen Zhi-Min, Zhang Huang, Luo Zhong-Ling

机构信息

Department of Ophthalmology, Zhongshan Torch Development Zone People's Hospital, Zhongshan, People's Republic of China.

出版信息

Clin Med Insights Case Rep. 2024 May 14;17:11795476241254266. doi: 10.1177/11795476241254266. eCollection 2024.

DOI:10.1177/11795476241254266
PMID:38751963
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11095178/
Abstract

Meige syndrome is a rare neurological disease characterized by segmental dystonia, specifically blepharospasm and oromandibular dystonia. These symptoms are often accompanied by complex movements of the eyelids, lower facial muscles, mandible, and neck muscles. Bilateral blepharospasm is the most common feature of this disease. In this case report, we present the successful treatment of refractory blepharospasm in a 72-year-old woman with Meige syndrome via 2 incisions resulting from myectomy and in situ surgery.

摘要

梅杰综合征是一种罕见的神经疾病,其特征为节段性肌张力障碍,具体表现为眼睑痉挛和口下颌肌张力障碍。这些症状常伴有眼睑、面部下部肌肉、下颌和颈部肌肉的复杂运动。双侧眼睑痉挛是该疾病最常见的特征。在本病例报告中,我们介绍了通过肌切除术和原位手术的两个切口成功治疗一名72岁梅杰综合征女性患者难治性眼睑痉挛的情况。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/76b3/11095178/47b6352c9d51/10.1177_11795476241254266-fig2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/76b3/11095178/7a0177ad7fea/10.1177_11795476241254266-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/76b3/11095178/47b6352c9d51/10.1177_11795476241254266-fig2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/76b3/11095178/7a0177ad7fea/10.1177_11795476241254266-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/76b3/11095178/47b6352c9d51/10.1177_11795476241254266-fig2.jpg

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本文引用的文献

1
The long-term response to botulinum toxin injections in patients with blepharospasm undergoing upper eyelid surgery.眼睑痉挛患者行上眼睑手术中接受肉毒毒素注射的长期反应。
Parkinsonism Relat Disord. 2024 Feb;119:105958. doi: 10.1016/j.parkreldis.2023.105958. Epub 2023 Dec 15.
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Multiple system atrophy associated with Meige syndrome: A rare case report.多系统萎缩合并梅杰综合征:一例罕见病例报告。
Radiol Case Rep. 2023 Jun 29;18(9):3192-3195. doi: 10.1016/j.radcr.2023.04.055. eCollection 2023 Sep.
3
Selective Myectomy and Myotomy In Situ for the Management of Refractory Blepharospasm in Meige Syndrome.
选择性原位肌切除术和肌切开术治疗梅杰综合征难治性眼睑痉挛
Ann Plast Surg. 2023 Apr 1;90(1 Suppl 1):S84-S88. doi: 10.1097/SAP.0000000000003367. Epub 2023 Jan 18.
4
Refractory dry eye disease associated with Meige's syndrome induced by long-term use of an atypical antipsychotic.与梅格综合征相关的难治性干眼症,由长期使用非典型抗精神病药物引起。
BMC Ophthalmol. 2020 Dec 2;20(1):474. doi: 10.1186/s12886-020-01738-w.
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A Case of Meige Syndrome Treated With Baclofen.1例用巴氯芬治疗的梅杰综合征病例
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Myotomy In Situ for Essential Blepharospasm Refractory to Botulinum Toxin.肉毒杆菌毒素治疗无效的原发性睑痉挛原位肌切开术
Ann Plast Surg. 2020 Jan;84(1S Suppl 1):S74-S79. doi: 10.1097/SAP.0000000000002182.
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Meige Syndrome Related to Vortioxetine in 2 Sisters: Case Reports.两姐妹中与伏硫西汀相关的梅杰综合征:病例报告
J Clin Psychopharmacol. 2019 Nov/Dec;39(6):679-681. doi: 10.1097/JCP.0000000000001108.
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Surgical Myectomy for Essential Blepharospasm and Hemifacial Spasm.手术性肌切除术治疗特发性眼睑痉挛和半面痉挛。
Int Ophthalmol Clin. 2018 Winter;58(1):63-70. doi: 10.1097/IIO.0000000000000206.
9
Meige's syndrome: History, epidemiology, clinical features, pathogenesis and treatment.梅杰综合征:历史、流行病学、临床特征、发病机制与治疗
J Neurol Sci. 2017 Jan 15;372:162-170. doi: 10.1016/j.jns.2016.11.053. Epub 2016 Nov 23.
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