Chan Lap Kei, Ho Ho Yin, Yu Chi Shing
Kwai Chung Hospital, Hong Kong.
Innov Clin Neurosci. 2012 Jul;9(7-8):39-41.
Meige syndrome is a rare form of segmental dystonia characterized by blepharospasm and oromandibular dystonia. A few case reports of Meige syndrome have been associated with Lewy body pathologies, and the syndrome was also proposed for inclusion in the spectrum of Lewy body disease. We report a case of an elderly gentleman with a history of Meige syndrome for more than 10 years who developed dementia with Lewy bodies. Updated clinical and pathological evidence of linkages between these two conditions is also presented.
梅杰综合征是节段性肌张力障碍的一种罕见形式，其特征为眼睑痉挛和口下颌肌张力障碍。少数梅杰综合征病例报告与路易体病变有关，该综合征也被提议纳入路易体病谱。我们报告一例有超过10年梅杰综合征病史的老年男性患者，其发展为路易体痴呆。本文还展示了这两种疾病之间关联的最新临床和病理证据。
