Hamid Mohamed, Slimani Sara, Alloussi Houda, Bourazza Ahmad
Department of Neurology, Mohammed V Military Instruction Hospital, Rabat 10000, Morocco.
Radiol Case Rep. 2024 Jun 17;19(9):3724-3728. doi: 10.1016/j.radcr.2024.05.044. eCollection 2024 Sep.
Multiple system atrophy is a form of synucleinopathy with an unknown etiology that causes progressive neurodegeneration. It may affect the cerebellum, autonomic nerves, and pyramidal and extrapyramidal systems. We present the case of a 51-year-old man who was hospitalized for recurrent balance problems and dizziness. Cranial magnetic resonance imaging showed the "hot cross bun" sign of the pons with major atrophy of the cerebellum. The cerebellar form of probable multiple system atrophy was the final diagnosis.
多系统萎缩是一种病因不明的突触核蛋白病,可导致进行性神经变性。它可能影响小脑、自主神经以及锥体和锥体外系。我们报告一例51岁男性患者,因反复出现平衡问题和头晕而住院。头颅磁共振成像显示脑桥的“热十字面包”征以及小脑严重萎缩。最终诊断为可能的小脑型多系统萎缩。