Helou Maroun, Al Irr Nael
General Practice, Faculty of Medicine and Health Science, An-Najah National University, Nablus, PSE.
Internal Medicine, Palestine Medical Complex, Ramallah, PSE.
Cureus. 2024 Jun 17;16(6):e62548. doi: 10.7759/cureus.62548. eCollection 2024 Jun.
Behcet's disease (BD) is an uncommon, long-term inflammatory condition characterized by recurring ulcers in the mouth and genital area, uveitis, and various systemic issues. One of the particularly rare but severe complications of this disease is the formation of pulmonary artery aneurysms (PAAs). Although these aneurysms are uncommon, they can lead to dangerous pulmonary hemorrhages (PHs), which are often fatal, requiring prompt diagnosis and intervention. We present a case of lower segment PAA in an 18-year-old patient with recently diagnosed BD, presenting with life-threatening PH and managed successfully with microcoil embolization of the aneurysm and immunosuppressive (IS) medications, achieving stable remission without complications.
白塞病(BD)是一种罕见的长期炎症性疾病,其特征为口腔和生殖器反复出现溃疡、葡萄膜炎以及各种全身性问题。该疾病一种特别罕见但严重的并发症是肺动脉瘤(PAA)的形成。尽管这些动脉瘤并不常见,但它们可导致危险的肺出血(PH),而肺出血往往是致命的,需要及时诊断和干预。我们报告一例18岁近期诊断为白塞病的患者发生下段PAA的病例,该患者出现危及生命的肺出血,通过动脉瘤微线圈栓塞和免疫抑制(IS)药物治疗成功治愈,实现稳定缓解且无并发症。