弥漫性头皮神经纤维瘤：病例系列及一种罕见血管病变的临床放射学特征
Diffuse scalp neurofibromas: Case series and Clinicoradiological characteristics of a rare vascular lesion.
作者信息
Bleakley Aaron, Betts Guy, Sainuddin Sajid, Hilditch Christopher
机构信息
Royal Salford Hospital Manchester Centre for Clinical Neurosciences, UK.
Manchester University NHS Foundation Trust, UK.
出版信息
Interv Neuroradiol. 2024 Aug 2:15910199241267301. doi: 10.1177/15910199241267301.
Abstract
Diffuse neurofibroma of the head and neck are rare tumours which have unique clinical and radiological findings. Presurgical diagnosis is important as these lesions are usually highly vascular and pre-operative embolisation can reduce the risk of intra-operative haemorrhage. In this article we describe four cases; two which underwent pre-operative embolisation, which should aid the reader in successfully diagnosing this entity before biopsy/surgery.
摘要
头颈部弥漫性神经纤维瘤是一种罕见肿瘤，具有独特的临床和放射学表现。术前诊断很重要，因为这些病变通常血管丰富，术前栓塞可降低术中出血风险。在本文中，我们描述了4例病例；其中2例接受了术前栓塞，这将有助于读者在活检/手术前成功诊断该疾病。
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