Belenky V V, Plakhotina N A, Dugaev P A, Komantsev V N
LLC Arsvita Clinic, St. Petersburg, Russia.
LLC «Sergey Berezin Medical Institute», St. Petersburg, Russia.
Zh Nevrol Psikhiatr Im S S Korsakova. 2024;124(8. Vyp. 2):47-50. doi: 10.17116/jnevro202412408247.
The Foix-Alajouanine syndrome was originally reported by these authors in 1926, as rapidly progressive vasculitis on the background of a viral infection. The pathology was represented by the huge, more than 10 times, dilation either of the lumen, or the walls of the spinal vessels, either of the arteries, or the veins. There were no signs of thrombosis, no malformations. Massive necrosis was observed in the spinal cord. Though plenty of observations of the syndrome were reported over the past 100 years, most of them deal with arteriovenous malformations and/or thrombosis, which had not been revealed originally. We present the case of spinal viral vasculitis detected by means of spinal MR-angiography. The undoubted viral etiology of vasculitis allows us to attribute this observation to Foix-Alajouanine syndrome.
福瓦-阿亚琼综合征最初由这些作者于1926年报道，表现为病毒感染背景下的快速进展性血管炎。病理学表现为脊髓血管（动脉或静脉）管腔或血管壁巨大扩张，超过10倍。未见血栓形成迹象，无畸形。脊髓出现大片坏死。尽管在过去100年里有大量关于该综合征的报道，但大多数涉及动静脉畸形和/或血栓形成，而这些最初并未被发现。我们报告一例通过脊髓磁共振血管造影检测到的脊髓病毒性血管炎病例。血管炎明确的病毒病因使我们将此病例归为福瓦-阿亚琼综合征。
