Wang Yahong, Dong Yifan, Tian Xueyu, Chen Yu, Yang Xiao, Li Jianchu
Department of Medical Ultrasound, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China.
Department of Ultrasound, Tianjin Wuqing District Hospital of Traditional Chinese Medicine, Tianjin, China.
Front Med (Lausanne). 2024 Aug 13;11:1422652. doi: 10.3389/fmed.2024.1422652. eCollection 2024.
Intravenous leiomyomatosis (IVL) is a rare gynecological-related tumor. It can invade and extend in the blood vessel and eventually involve the cardiac cavity or even the pulmonary artery. IVL generally does not adhere to the vein wall and infrequently leads to the manifestation of Budd-Chiari syndrome (BCS). In this case report, the presence of a sizable tumor obstructed the second hepatic portal, impeding the return flow of the hepatic veins, thereby precipitating the development of BCS. The presence of collateral veins and dilation of the accessory hepatic vein were identified through computed tomography venography and ultrasonography, thus supporting the diagnosis of BCS. The patient underwent a comprehensive surgical resection and was found to have a favorable prognosis.
静脉内平滑肌瘤病（IVL）是一种罕见的妇科相关肿瘤。它可在血管内侵袭和蔓延，最终累及心腔甚至肺动脉。IVL通常不附着于静脉壁，很少导致布加综合征（BCS）的表现。在本病例报告中，一个较大的肿瘤阻塞了第二肝门，阻碍了肝静脉的回流，从而引发了BCS的发展。通过计算机断层扫描静脉造影和超声检查发现了侧支静脉的存在以及副肝静脉的扩张，从而支持了BCS的诊断。患者接受了全面的手术切除，预后良好。
