El Mohtarim Rihane, Sassi Samia, El Ansari Nawal, Rguieg Naji, El Ghafouli Sara, Rouas Lamiaa, Lamalmi Najat
Department of Pathology, Ibn Sina Teaching Hospital, Abderrahim Bouabid Avenue, Rabat 12000, Morocco.
Mohamed V University, Nations unie Avenue, Rabat 12000, Morocco.
J Surg Case Rep. 2024 Oct 2;2024(10):rjae606. doi: 10.1093/jscr/rjae606. eCollection 2024 Oct.
Epithelioid sarcoma (ES) is a rare soft tissue tumor that is commonly misdiagnosed. It is a mesenchymal tumor that shows both mesenchymal and epithelial features. It tends to occur in the distal upper extremity in children and young adults but may appear in any location and any age group. Less than 1% of ES involve the head and neck. Clinically, the tumor can be mistakenly confused with a benign lesion as it can mimic nonspecific ulcers or infected warts. Histologically, ES is characterized by a nodular architecture and epithelioid appearance of cells centered with necrosis, mimicking a granulomatous process. We present the clinical history of a 12-year-old male who presented with an ES of the pretragus with a brief review of the literature to raise awareness on this rare entity and to discuss the challenges in managing histopathological differential diagnosis in front of this unusual clinical presentation.
上皮样肉瘤（ES）是一种罕见的软组织肿瘤，常被误诊。它是一种间叶性肿瘤，兼具间叶和上皮特征。它倾向于发生在儿童和年轻成人的上肢远端，但也可能出现在任何部位和任何年龄组。不到1%的上皮样肉瘤累及头颈部。临床上，该肿瘤可能被误诊为良性病变，因为它可类似非特异性溃疡或感染性疣。组织学上，上皮样肉瘤的特征是呈结节状结构，细胞呈上皮样外观，中心有坏死，类似肉芽肿过程。我们介绍一名12岁男性患者的临床病史，该患者患有耳前上皮样肉瘤，并简要回顾文献，以提高对这一罕见疾病的认识，并讨论面对这种不寻常临床表现时在组织病理学鉴别诊断管理方面的挑战。
