Patil Vaibhavi, Deshmukh Prasad, Gaurkar Sagar S, Ghosh Moulic Ayushi, Kaur Jasleen
Otolaryngology - Head and Neck Surgery, Jawaharlal Nehru Medical College, Datta Meghe Institute of Higher Education & Research, Wardha, IND.
Cureus. 2024 Sep 4;16(9):e68676. doi: 10.7759/cureus.68676. eCollection 2024 Sep.
Hemangiopericytomas (HPCs) are rare vascular tumors originating from pericytes, with a predilection for the musculoskeletal system and occasional occurrence in the head and neck region. HPCs arising in the external auditory canal (EAC) are exceptionally rare, making their diagnosis and management a clinical challenge. A 71-year-old male presented with a six-month history of a painless, progressively enlarging mass in his right EAC, accompanied by tinnitus and hearing loss. Physical examination revealed a mobile, reddish mass in the concha of the left auricle, nearly occluding the EAC. Contrast-enhanced computed tomography of the temporal bone demonstrated a heterogeneously enhancing mass with erosion of adjacent structures. Histopathological examination and immunohistochemistry confirmed the diagnosis of an HPC. The tumor was surgically excised, and the patient underwent adjuvant radiotherapy. Over a two-year follow-up period, no recurrence was observed. This case highlights the rarity of HPCs in the EAC and underscores the importance of considering this diagnosis in patients presenting with atypical EAC masses. A multidisciplinary approach, including surgical excision and radiotherapy, is crucial for achieving favorable outcomes and reducing the risk of recurrence. Long-term follow-up is essential due to the potential for late recurrence.
血管外皮细胞瘤（HPCs）是一种起源于周细胞的罕见血管肿瘤，好发于肌肉骨骼系统，偶尔发生于头颈部区域。发生于外耳道（EAC）的HPCs极为罕见，其诊断和治疗是一项临床挑战。一名71岁男性患者，右外耳道有无痛性、进行性增大肿物6个月病史，伴有耳鸣和听力减退。体格检查发现左耳甲腔有一可活动的红色肿物，几乎阻塞外耳道。颞骨增强计算机断层扫描显示肿物呈不均匀强化，伴有相邻结构侵蚀。组织病理学检查和免疫组化确诊为HPC。肿瘤经手术切除，患者接受辅助放疗。在两年的随访期内，未观察到复发。该病例凸显了外耳道HPCs的罕见性，并强调了对于表现为非典型外耳道肿物的患者考虑这一诊断的重要性。多学科方法，包括手术切除和放疗，对于取得良好预后和降低复发风险至关重要。由于存在晚期复发的可能性，长期随访必不可少。
