Dawadi Kapil, Dahal Prajwal, Upadhyaya Rudra Prasad, Poudyal Binuda
Department of Radiology and Imaging, Grande International Hospital, Kathmandu, Nepal.
Department of Pediatrics, Grande International Hospital, Kathmandu, Nepal.
Radiol Case Rep. 2024 Nov 14;20(1):777-780. doi: 10.1016/j.radcr.2024.10.078. eCollection 2025 Jan.
Hypogenetic lung syndrome, commonly known as Scimitar syndrome, is a rare cardiopulmonary anomaly characterized primarily by anomalous pulmonary venous return and lung hypoplasia. While it is most frequently diagnosed in infancy or early childhood, cases in adulthood are exceedingly rare. We present a case of a middle-aged female who was diagnosed with Scimitar syndrome.
肺发育不全综合征,通常称为弯刀综合征,是一种罕见的心肺异常,主要特征为肺静脉回流异常和肺发育不全。虽然它最常在婴儿期或幼儿期被诊断出来,但成年期病例极为罕见。我们报告一例中年女性被诊断为弯刀综合征的病例。