Verma Damini, Sarkar Rashmi, Mendiratta Vibhu, Srivastava Amol
From the Department of Dermatology, Lady Hardinge Medical College and Hospitals, Connaught Place, New Delhi, India.
Department of Radiology, Institute of Liver and Biliary Sciences, New Delhi, India.
Indian J Dermatol. 2024 Sep-Oct;69(5):422. doi: 10.4103/ijd.ijd_234_23. Epub 2024 Oct 29.
Skin colour usually depends upon melanin, haemoglobin, and carotenoids. Pigmentary disorders indicate an increased amount of melanin, leading to a darker colour of the skin, called hypermelanosis. Addison's disease is a rare endocrinal disorder with severe oral and systemic manifestations. Any form of diffuse skin hyper-pigmentation which is more pronounced on sun-exposed areas mimics Addison's disease and is called Addisonian pigmentation. Pigmentation often precedes other manifestations by months to years and hence can lead to early diagnosis and can prevent life-threatening adrenal crisis. The most common cause of adrenal insufficiency in developing countries is tuberculosis. A similar pattern of pigmentation has been reported in Cushing's syndrome, ectopic ACTH-producing tumours, vitamin B12 deficiency, and thyrotoxicosis. Addisonian pigmentation can be a manifestation of multiple systemic diseases; hence, an inter-disciplinary approach is needed with extensive clinical and laboratory evaluation. It is not merely a cosmetic concern. Not much data are available in the literature regarding this entity. This brief review serves as an important source for clinicians to stay up-to-date regarding the history, clinical presentation, differential diagnosis, and management of this entity.
皮肤颜色通常取决于黑色素、血红蛋白和类胡萝卜素。色素沉着紊乱表明黑色素含量增加,导致皮肤颜色加深,称为色素沉着过度。艾迪生病是一种罕见的内分泌紊乱疾病,具有严重的口腔和全身表现。任何形式的弥漫性皮肤色素沉着在暴露于阳光下的部位更为明显,类似于艾迪生病,称为艾迪生病样色素沉着。色素沉着通常比其他表现提前数月至数年出现,因此可导致早期诊断并预防危及生命的肾上腺危象。发展中国家肾上腺功能不全最常见的原因是结核病。在库欣综合征、异位促肾上腺皮质激素分泌肿瘤、维生素B12缺乏症和甲状腺毒症中也报告了类似的色素沉着模式。艾迪生病样色素沉着可能是多种全身性疾病的表现;因此,需要采取跨学科方法进行广泛的临床和实验室评估。这不仅仅是一个美容问题。关于这个实体的文献资料不多。这篇简短的综述是临床医生了解该实体的历史、临床表现、鉴别诊断和管理最新情况的重要来源。