Laizer Fred, Nkini Hanson, Babu Heri, Medard Erasto, Bamanyis Amon, Veronesi Teodros
Department of General Surgery, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, Tanzania.
Department of Histopathology, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, Tanzania.
Urol Case Rep. 2024 Nov 22;58:102887. doi: 10.1016/j.eucr.2024.102887. eCollection 2025 Jan.
Renal angiomyolipoma is an uncommon benign tumor that mostly affects adults and is highly associated with tuberous sclerosis. It's very uncommon for it to affect adolescents. In this case, a 17-year-old male with abdominal pain and distension was diagnosed with sporadic giant renal angiomyolipoma. Histopathology confirmed the diagnosis after a successful nephrectomy. Though rare in teenagers, giant renal angiomyolipoma can be managed with surgery. Histopathology is a mainstay of confirming the diagnosis.
This case highlights the difficulties in managing big retroperitoneal tumors in teenagers and the necessity of taking sporadic angiomyolipoma into account when making a differential diagnosis.
肾血管平滑肌脂肪瘤是一种罕见的良性肿瘤,主要影响成年人,且与结节性硬化症高度相关。它很少影响青少年。在本病例中,一名17岁腹痛腹胀男性被诊断为散发性巨大肾血管平滑肌脂肪瘤。组织病理学在成功肾切除术后确诊。尽管巨大肾血管平滑肌脂肪瘤在青少年中罕见,但可通过手术治疗。组织病理学是确诊的主要依据。
本病例凸显了青少年巨大腹膜后肿瘤管理的困难,以及在鉴别诊断时考虑散发性血管平滑肌脂肪瘤的必要性。