Martini A, Ravelli A, Notarangelo L D, Burgio V L, Plebani A
Arch Dis Child. 1985 Feb;60(2):160-2. doi: 10.1136/adc.60.2.160.
A 9 year old girl presented with clinical manifestations of Henoch-Schönlein syndrome and macroscopic haematuria. Laboratory investigations showed selective IgA deficiency and renal biopsy showed mesangial proliferative glomerulonephritis with diffuse granular deposits of C3 on immunofluorescence. IgA deposits were absent.
一名9岁女孩出现了过敏性紫癜的临床表现及肉眼血尿。实验室检查显示选择性IgA缺乏,肾活检显示系膜增生性肾小球肾炎,免疫荧光检查可见C3呈弥漫性颗粒状沉积。IgA沉积缺如。