Calò Leonardo, Toto Federica, Panattoni Germana, Romeo Fabiana, Fusco Armando, Stefanini Matteo, Silvetti Elisa, Martino Annamaria, Fedele Elisa, Danza Ludovica, Lanzillo Chiara, Canestrelli Stefano, Canali Emanuele, Ciampi Pellegrino, Politano Alessandro, Crescenzi Cinzia
Division of Cardiology, Policlinico Casilino, Via Casilina 1049, 00169 Rome, Italy.
Department of Motor, Human and Health Sciences, "Foro Italico", University of Rome, Italy.
Eur Heart J Suppl. 2025 Feb 19;27(Suppl 1):i83-i87. doi: 10.1093/eurheartjsupp/suae110. eCollection 2025 Feb.
Electrocardiogram (ECG) may play a crucial role in the diagnosis of left-sided variants of desmosomal arrhythmogenic cardiomyopathies. This article discusses the most common ECG changes, such as T-wave inversion and low QRS voltages, and new ECG signs such as Q-waves, low voltages in specific leads, posterior fascicle block, and R/S ratio ≥ 0.5 in V1. In addition, ventricular arrhythmias have peculiar features in these patients. Electrocardiogram may be an early marker of this insidious cardiomyopathy and allow to avoid sudden cardiac death often in young people. Electrocardiogram abnormalities may also be indicators of disease evolution over time.
心电图(ECG)在诊断桥粒性致心律失常性心肌病的左侧变异型中可能起关键作用。本文讨论了最常见的心电图变化,如T波倒置和QRS波低电压,以及新的心电图征象,如Q波、特定导联低电压、后分支阻滞和V1导联R/S比值≥0.5。此外,这些患者的室性心律失常具有特殊特征。心电图可能是这种隐匿性心肌病的早期标志物,并常常能使年轻人避免心源性猝死。心电图异常也可能是疾病随时间演变的指标。