一例成人致心律失常性右室心肌病病例。

An adult case of arrhythmogenic right ventricular dysplasia.

作者信息

Yasuda M, Akioka K, Teragaki M, Komatsu H, Inoue E, Minamikawa H, Kotsumi K, Yoshimura T, Ikuno Y, Oku H

出版信息

Jpn Heart J. 1985 Jan;26(1):127-32. doi: 10.1536/ihj.26.127.

DOI:10.1536/ihj.26.127

Abstract

A forty-year-old man was admitted to our hospital because of dizziness, palpitations and an oppressive feeling in the precordium. Physical examination was normal. A chest roentgenogram revealed mild cardiomegaly and the electrocardiogram showed ventricular tachycardia of a left bundle branch block configuration which was terminated by the intravenous injection of procainamide. During sinus rhythm the electrocardiogram showed incomplete right bundle branch block, PQ prolongation and inverted T waves in leads V1 through V3. Two-dimensional echocardiography revealed only moderate right ventricular dilatation. Right ventricular angiography showed severe right ventricular dilatation and hypokinesis of the right ventricular apex and pulmonary artery infundibulum. From these characteristics signs we concluded that this adult patient had arrhythmogenic right ventricular dysplasia (ARVD), suggesting that this condition is not confined to children but may occur in adults as well.

摘要

一名40岁男性因头晕、心悸和心前区压迫感入院。体格检查正常。胸部X线片显示轻度心脏扩大，心电图显示左束支阻滞形态的室性心动过速，静脉注射普鲁卡因胺后终止。窦性心律时，心电图显示不完全性右束支阻滞、PQ间期延长及V1至V3导联T波倒置。二维超声心动图仅显示中度右心室扩张。右心室造影显示严重右心室扩张，右心室尖部及肺动脉漏斗部运动减弱。根据这些特征性表现，我们得出结论，该成年患者患有致心律失常性右心室发育不良（ARVD），提示这种疾病不仅限于儿童，也可能发生于成人。