Condé Naomie, Carias Mathew, Pressacco Josephine
Department of Medicine, McGill University, 845 Sherbrooke W, Montreal (QC), H3A 0G4, Canada.
Department of Radiology, McGill University Health Center, 1001 Bd Décarie, Montreal (QC), H4A 3J1, Canada.
Oxf Med Case Reports. 2025 Mar 20;2025(3):omae209. doi: 10.1093/omcr/omae209. eCollection 2025 Mar.
Unilateral absence of the pulmonary artery is a congenital disorder resulting from malformation of the sixth aortic arch during embryogenesis. This case report presents a unique instance of unilateral absence of the pulmonary artery, incidentally discovered in an individual with multiple myeloma. Despite a history of recurrent childhood pulmonary infections, the patient remained asymptomatic until presenting with symptoms of myeloma. Imaging revealed a right-sided aortic arch, absent left pulmonary artery, and left lung atrophy with atelectasis. Among various collateral arteries, a notable finding in this case is the left gastric artery supplying the left lower lobe.
单侧肺动脉缺如是一种先天性疾病，由胚胎发育过程中第六对主动脉弓畸形引起。本病例报告呈现了一例单侧肺动脉缺如的独特病例，该病例在一名患有多发性骨髓瘤的个体中偶然发现。尽管患者童年时有反复肺部感染史，但在出现骨髓瘤症状之前一直无症状。影像学检查显示右侧主动脉弓、左肺动脉缺如以及左肺萎缩伴肺不张。在各种侧支动脉中，本病例的一个显著发现是左胃动脉为左下叶供血。
