Liang Hongqin, Kong Li, Liu Fei, Ji Xiaojuan, Zhang Nan, Wang Jian
Department of Radiology, Third Military Medical University Southwest Hospital (Army Medical University), Chongqing, China.
Department of Ultrasound, Children's Hospital of Chongqing Medical University, Chongqing, China.
BMC Cardiovasc Disord. 2025 Apr 2;25(1):248. doi: 10.1186/s12872-025-04659-y.
Criss-cross heart (CCH) is a rare congenital heart malformation characterized by twisted atrioventricular connections, often associated with various other cardiac anomalies, making accurate diagnosis challenging; In this article, we present a previously unreported case of CCH with complex cardiac malformation, situs inversus totalis, and bronchial dysplasia.
A 10-year-old girl presented with recurrent cyanosis and fatigue, and echocardiography revealed a complex congenital heart condition involving CCH, dextrocardia, severe pulmonary hypertension, ventricular septal defect (VSD), atrial septal defect (ASD), and patent ductus arteriosus (PDA). Further CT angiography unveiled bronchial dysplasia and double-outlet right ventricle (DORV).
CCH is a rare congenital heart condition characterized by twisted atrioventricular connections, with complex associated anomalies. Diagnosis is challenging due to the variety of defects. CT angiography is crucial for comprehensive assessment and surgical planning. This case presented a unique combination of CCH with mirror dextrocardia, situs inversus totalis, and bronchial malformation, highlighting the importance of CT in guiding treatment decisions. However, postoperative follow-up is lacking, and optimal surgical strategies for such complex deformities remain to be explored.
交叉心脏（CCH）是一种罕见的先天性心脏畸形，其特征为房室连接扭曲，常伴有各种其他心脏异常，这使得准确诊断具有挑战性；在本文中，我们报告了一例此前未报道的伴有复杂心脏畸形、完全性内脏反位和支气管发育不良的CCH病例。
一名10岁女孩出现反复发绀和疲劳，超声心动图显示患有包括CCH、右位心、严重肺动脉高压、室间隔缺损（VSD）、房间隔缺损（ASD）和动脉导管未闭（PDA）的复杂先天性心脏病。进一步的CT血管造影显示支气管发育不良和右心室双出口（DORV）。
CCH是一种罕见的先天性心脏病，其特征为房室连接扭曲，并伴有复杂的相关异常。由于缺陷种类繁多，诊断具有挑战性。CT血管造影对于全面评估和手术规划至关重要。该病例呈现了CCH与镜像右位心、完全性内脏反位和支气管畸形的独特组合，突出了CT在指导治疗决策中的重要性。然而，缺乏术后随访，此类复杂畸形的最佳手术策略仍有待探索。
