Soler Lisa M, Hambright Benjamin C, Pearce Benjamin J, Still Sasha A
Division of Cardiothoracic Surgery, University of Alabama at Birmingham, Birmingham, AL.
Heersink School of Medicine, University of Alabama at Birmingham, Birmingham, AL.
J Vasc Surg Cases Innov Tech. 2025 Mar 8;11(3):101779. doi: 10.1016/j.jvscit.2025.101779. eCollection 2025 Jun.
Open replacement of multifocal aortic aneurysms is an operative and clinical challenge. Thoughtful consideration of both surgical technique and timing is important to reduce risk of major cardiovascular and neurologic complications. We discuss the management of a 34-year-old male with suspected connective tissue disease admitted with multifocal, giant aneurysms of his right subclavian artery, ascending and aortic arch, descending and abdominal aorta, and right iliac artery. A complex, open three-stage repair was undertaken. Genetic testing revealed a missense MYH11 mutation. We describe our approach and patient outcome.
多灶性主动脉瘤的开放置换术是一项手术和临床挑战。仔细考虑手术技术和时机对于降低重大心血管和神经并发症的风险很重要。我们讨论了一名34岁疑似结缔组织病男性患者的治疗情况，该患者因右锁骨下动脉、升主动脉和主动脉弓、降主动脉和腹主动脉以及右髂动脉的多灶性巨大动脉瘤入院。进行了复杂的开放三阶段修复。基因检测发现了一个错义MYH11突变。我们描述了我们的治疗方法和患者的预后情况。
