Flores-Olmos Nora Lis, Hernández-Álvarez Francisco Javier, Frausto-Luján Ricardo, Valencia-Romero Montserrat Del Carmen
Instituto de Seguridad y Servicios Sociales de los Trabajadores del Estado, Hospital Regional "Valentín Gómez Farias", Servicio de Cirugía General. Zapopan, Jalisco, México.
Secretaría de Salud, Hospital Civil de Oaxaca "Aurelio Valdivieso", Servicio de Cirugía General. Oaxaca, Oaxaca, México.
Rev Med Inst Mex Seguro Soc. 2025 Jan 3;63(1):e6394. doi: 10.5281/zenodo.14201190.
Intestinal malrotation is a congenital anomaly resulting from abnormal rotation of the intestine during fetal development, affecting its fixation and orientation. Although it is primarily diagnosed in infancy, it can cause severe complications in adults, such as intestinal obstruction, volvulus, and perforation. The objective is to illustrate the clinical presentation and management of intestinal malrotation in adults, highlighting the complications and the importance of early diagnosis.
53-year-old man with generalized abdominal distension and pain, nausea, vomiting, and absence of bowel movements. Computed tomography (CT) revealed free air and fluid in the abdominal cavity, suggesting intestinal perforation. Surgery revealed cecal perforation, necrosis of the ascending colon, and a characteristic malrotation pattern. A right hemicolectomy, resection of affected intestinal segments, and creation of a terminal ileostomy were performed.
Intestinal malrotation in adults can present with nonspecific symptoms, complicating its diagnosis. Secondary obstruction can lead to increased intraluminal pressure, ischemia, and perforation. Perforation, resulting from prolonged obstruction, requires early diagnosis with CT. Urgent surgical intervention is essential to repair the perforation and the intestinal malrotation. The Ladd procedure is the standard treatment to correct malrotation and prevent future complications.
肠旋转不良是一种先天性异常,由胎儿发育期间肠道异常旋转引起,影响其固定和方向。虽然它主要在婴儿期被诊断出来,但它可在成人中引起严重并发症,如肠梗阻、肠扭转和穿孔。目的是阐述成人肠旋转不良的临床表现和管理,强调并发症以及早期诊断的重要性。
一名53岁男性,有全身腹胀、疼痛、恶心、呕吐,且无排便。计算机断层扫描(CT)显示腹腔内有游离气体和液体,提示肠穿孔。手术发现盲肠穿孔、升结肠坏死以及典型的旋转不良模式。进行了右半结肠切除术、切除受影响的肠段并做了末端回肠造口术。
成人肠旋转不良可表现为非特异性症状,使其诊断复杂化。继发性梗阻可导致管腔内压力升高、缺血和穿孔。由长期梗阻导致的穿孔需要通过CT进行早期诊断。紧急手术干预对于修复穿孔和纠正肠旋转不良至关重要。Ladd手术是纠正旋转不良并预防未来并发症的标准治疗方法。