Department of Surgery, University of California San Francisco, 505 Parnassus Ave, San Francisco, CA, 94143, USA.
Department of Surgery, California Pacific Medical Center, San Francisco, CA, USA.
BMC Surg. 2022 Jan 29;22(1):35. doi: 10.1186/s12893-022-01482-6.
Malrotation with bowel ischemia is classically thought of as a disease of infants. However, the true prevalence of malrotation in both the pediatric and adult population is unknown due to the unclear number of asymptomatic patients.
A previously healthy 84-year-old man with no prior abdominal surgeries presented with an acute abdomen and was found on CT to have small bowel located in the right hemiabdomen and an abnormal SMA-SMV relationship suggestive of intestinal malrotation, as well as pneumatosis intestinalis. He underwent an exploratory laparotomy, where he was found to have a paraduodenal space which did not contain any bowel but was the likely source of an internal hernia. His duodenojejunal flexure was located to the right of the spinal column, the cecum in the left lower quadrant, a thick congenital band at the proximal jejunum, and multiple Ladd's bands at the level of the duodenum. The bowel appeared viable and a Ladd's procedure was performed. The patient had an uneventful post-operative course.
There is a lack of guidelines regarding screening for and management of asymptomatic malrotation in older children and adults. However, the traditional thinking is that asymptomatic malrotation diagnosed after two years of age poses minimal risk. This case illustrates the potential risk of an internal hernia in the setting of malrotation at any time during one's lifetime.
肠缺血性肠旋转不良通常被认为是一种婴儿疾病。然而,由于无症状患者的数量不清楚,小儿和成人人群中肠旋转不良的真实患病率尚不清楚。
一位先前健康的 84 岁男性,无腹部手术史,因急性腹痛就诊,CT 检查发现小肠位于右半腹部,肠系膜上动脉-肠系膜下动脉关系异常,提示肠旋转不良,以及肠壁积气。他接受了剖腹探查术,发现有十二指肠旁间隙,但没有任何肠管,可能是内疝的来源。他的十二指肠空肠曲位于脊柱右侧,盲肠位于左下腹,空肠近端有一条厚的先天性带,十二指肠水平有多条 Ladd 带。肠管外观有活力,行 Ladd 手术。患者术后恢复顺利。
对于较大儿童和成人无症状肠旋转不良的筛查和处理尚无指南。然而,传统观点认为,2 岁以后诊断的无症状肠旋转不良风险极小。本病例说明了在任何年龄段,肠旋转不良都可能导致内疝的潜在风险。