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纯合子镰状细胞病中的复发性视力丧失

Recurrent visual loss in homozygous sickle cell disease.

作者信息

Condon P I, Whitelocke R A, Bird A C, Talbot J F, Serjeant G R

出版信息

Br J Ophthalmol. 1985 Sep;69(9):700-6. doi: 10.1136/bjo.69.9.700.

DOI:10.1136/bjo.69.9.700
PMID:4041417
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1040714/
Abstract

In sickle cell retinopathy vascular involvement is most frequently recognised at the retinal periphery, but obstruction of perimacular arterioles and of major retinal vessels may also occur. This report describes a patient with homozygous sickle cell (SS) disease with recurrent occlusion of major retinal vessels associated with recurring transient impairment of visual function.

摘要

在镰状细胞视网膜病变中,血管受累最常出现在视网膜周边,但黄斑周围小动脉和主要视网膜血管也可能发生阻塞。本报告描述了一名纯合子镰状细胞(SS)病患者,其主要视网膜血管反复阻塞,并伴有反复短暂性视功能损害。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/8ae18e07eaac/brjopthal00141-0069-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/4759f38b8c15/brjopthal00141-0064-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/721f77650c0c/brjopthal00141-0065-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/44236e09ed6b/brjopthal00141-0066-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/18016215c88b/brjopthal00141-0066-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/ddede096ffc3/brjopthal00141-0067-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/f39baebc6d2a/brjopthal00141-0067-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/f6c1a0770ed5/brjopthal00141-0068-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/e03e9a90c096/brjopthal00141-0068-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/8ae18e07eaac/brjopthal00141-0069-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/4759f38b8c15/brjopthal00141-0064-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/721f77650c0c/brjopthal00141-0065-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/44236e09ed6b/brjopthal00141-0066-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/18016215c88b/brjopthal00141-0066-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/ddede096ffc3/brjopthal00141-0067-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/f39baebc6d2a/brjopthal00141-0067-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/f6c1a0770ed5/brjopthal00141-0068-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/e03e9a90c096/brjopthal00141-0068-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35a5/1040714/8ae18e07eaac/brjopthal00141-0069-a.jpg

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引用本文的文献

1
New classification of peripheral retinal vascular changes in sickle cell disease.镰状细胞病周边视网膜血管改变的新分类
Br J Ophthalmol. 1994 Sep;78(9):681-9. doi: 10.1136/bjo.78.9.681.

本文引用的文献

1
Salmon-patch hemorrhages after central retinal artery occlusion in sickle cell disease.镰状细胞病患者视网膜中央动脉阻塞后出现鲑鱼斑状出血。
Arch Ophthalmol. 1981 Feb;99(2):237-40. doi: 10.1001/archopht.1981.03930010239002.
2
Central retinal artery occlusion without retrobulbar hemorrhage after retrobulbar anesthesia.球后麻醉后发生中央视网膜动脉阻塞且无球后出血
Am J Ophthalmol. 1982 May;93(5):573-7. doi: 10.1016/s0002-9394(14)77371-4.
3
Macular vasculature, visual acuity, and irreversibly sickled cells in homozygous sickle cell disease.
纯合子镰状细胞病中的黄斑血管、视力及不可逆镰状细胞
Br J Ophthalmol. 1982 Mar;66(3):155-60. doi: 10.1136/bjo.66.3.155.
4
Isolated macular infarction in sickle cell (SS) disease.
Am J Ophthalmol. 1972 Jun;73(6):857-9. doi: 10.1016/0002-9394(72)90452-7.
5
Ocular findings in homozygous sickle cell anemia in Jamaica.牙买加纯合子镰状细胞贫血的眼部表现
Am J Ophthalmol. 1972 Apr;73(4):533-43. doi: 10.1016/0002-9394(72)90005-0.
6
Peripapillary and macular vessel occlusions in sickle cell anemia.
Am J Ophthalmol. 1973 May;75(5):861-6. doi: 10.1016/0002-9394(73)90892-1.
7
Sickling hemoglobinopathies; macular and perimacular vascular abnormalities.镰状血红蛋白病;黄斑及黄斑周围血管异常。
Arch Ophthalmol. 1974 Dec;92(6):455-63. doi: 10.1001/archopht.1974.01010010469002.
8
Multiple major retinal vascular occlusions in sickle cell haemoglobin C disease.镰状细胞血红蛋白C病中的多发性主要视网膜血管阻塞
Br J Ophthalmol. 1975 Sep;59(9):493-6. doi: 10.1136/bjo.59.9.493.
9
Macular and perimacular vascular remodelling sickling haemoglobinopathies.黄斑及黄斑周围血管重塑与镰状血红蛋白病
Br J Ophthalmol. 1976 Jun;60(6):431-53. doi: 10.1136/bjo.60.6.431.