Shiozawa Z, Ueda R, Mano T, Tsugane R, Kageyama N
J Neurol. 1985;232(5):280-2. doi: 10.1007/BF00313866.
A case of superior sagittal sinus thrombosis associated with Evans' syndrome of immune haemolytic anaemia is reported. The neurological symptoms and signs were headaches, right quadrant hemianopia, dyslexia without agraphia, motor aphasia, numbness in and weakness of the right upper extremity, papilloedema and coma. The cerebral venous sinus thrombosis, involving cerebral veins, superior sagittal sinus and straight sinus, was diagnosed by cerebral angiography. It is noteworthy that the superior sagittal sinus thrombosis occurred during a haematological recovery period, with rapid responses to treatment with 6-mercaptopurine and high doses of adrenocorticosteroids. Following a reduction in the doses of these drugs, the symptoms and signs related to the superior sagittal sinus thrombosis gradually subsided, and the haematological pictures remained in remission.
报告了一例与免疫性溶血性贫血的埃文斯综合征相关的上矢状窦血栓形成病例。神经症状和体征包括头痛、右侧象限偏盲、失读不伴失写、运动性失语、右上肢麻木和无力、视乳头水肿及昏迷。通过脑血管造影诊断为累及脑静脉、上矢状窦和直窦的脑静脉窦血栓形成。值得注意的是，上矢状窦血栓形成发生在血液学恢复期，对6-巯基嘌呤和高剂量肾上腺皮质类固醇治疗反应迅速。在这些药物剂量减少后，与上矢状窦血栓形成相关的症状和体征逐渐消退，血液学表现仍处于缓解状态。
