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心脏磁共振成像在非缺血性心肌病评估与管理中的应用

Cardiac Magnetic Resonance in the Evaluation and Management of Nonischemic Cardiomyopathies.

作者信息

Hosadurg Nisha, Lozano Patricia Rodriguez, Patel Amit R, Kramer Christopher M

机构信息

Department of Medicine, Cardiovascular Division, University of Virginia, Charlottesville, Virginia, USA; Department of Radiology and Medical Imaging, University of Virginia, Charlottesville, Virginia, USA.

Department of Medicine, Cardiovascular Division, University of Virginia, Charlottesville, Virginia, USA; Department of Radiology and Medical Imaging, University of Virginia, Charlottesville, Virginia, USA.

出版信息

JACC Heart Fail. 2025 Sep;13(9):102525. doi: 10.1016/j.jchf.2025.102525. Epub 2025 Jul 5.

DOI:10.1016/j.jchf.2025.102525
PMID:40618692
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12433598/
Abstract

Cardiac magnetic resonance is an essential tool in the evaluation and management of patients with suspected or diagnosed nonischemic cardiomyopathies (NICMs). It is considered the gold standard for accurately quantifying cardiac chamber dimensions, function, and mass, aiding in the initial diagnosis of myocardial dysfunction and/or dilation. Its unique value lies in its ability to characterize the myocardium using techniques such as late gadolinium enhancement, T1, T2, and T2∗ mapping, and extracellular volume fraction estimation, all of which have been histologically validated in specific clinical scenarios. These features enable specific diagnoses of the etiology of NICM, assess prognosis, guide management decisions, and potentially evaluate treatment response. This has allowed the widespread and increasing use of cardiac magnetic resonance in NICMs.

摘要

心脏磁共振成像(CMR)是评估和管理疑似或确诊的非缺血性心肌病(NICM)患者的重要工具。它被认为是准确量化心腔大小、功能和质量的金标准,有助于心肌功能障碍和/或扩张的初步诊断。其独特价值在于能够使用诸如延迟钆增强、T1、T2和T2*映射以及细胞外容积分数估计等技术来表征心肌,所有这些技术在特定临床场景中均已得到组织学验证。这些特性能够对NICM的病因进行特异性诊断、评估预后、指导管理决策并可能评估治疗反应。这使得心脏磁共振成像在NICM中得到广泛且日益增加的应用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/c29a95f1f1c5/nihms-2109783-f0006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/010a421e0fbd/nihms-2109783-f0003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/a7fbfdf9bd86/nihms-2109783-f0004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/80a41ab61f28/nihms-2109783-f0005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/c29a95f1f1c5/nihms-2109783-f0006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/010a421e0fbd/nihms-2109783-f0003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/a7fbfdf9bd86/nihms-2109783-f0004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/80a41ab61f28/nihms-2109783-f0005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201e/12433598/c29a95f1f1c5/nihms-2109783-f0006.jpg

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Rate of Change in Cardiac Magnetic Resonance Imaging Measures Is Associated With Death in Duchenne Muscular Dystrophy.心脏磁共振成像测量的变化率与杜氏肌营养不良症的死亡相关。
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