• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

先天性副肌强直症中小指展肌的收缩特性

Contractile properties of the abductor digiti minimi muscle in paramyotonia congenita.

作者信息

Burke D, Skuse N F, Lethlean A K

出版信息

J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):894-9. doi: 10.1136/jnnp.37.8.894.

DOI:10.1136/jnnp.37.8.894
PMID:4423558
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC494803/
Abstract

In two subjects with paramyotonia congenita the isometric torque generated by the abductor digiti minimi and the surface EMG recorded over ADM decreased during prolonged or repetitive contractions, whether these were voluntarily or electrically induced. Isometric twitch times did not alter significantly during this muscle fatigue. Cooling greatly accelerated the fatiguing process. It is suggested that this local muscle weakness is due to a progressive decrease in excitability of the muscle cell membrane.

摘要

在两名患有先天性副肌强直的受试者中,小指展肌产生的等长扭矩以及在小指展肌上记录的表面肌电图在长时间或重复收缩期间均下降,无论这些收缩是自愿诱发还是电诱发的。在这种肌肉疲劳过程中等长抽搐时间没有明显改变。冷却极大地加速了疲劳过程。提示这种局部肌肉无力是由于肌细胞膜兴奋性的逐渐降低所致。

相似文献

1
Contractile properties of the abductor digiti minimi muscle in paramyotonia congenita.先天性副肌强直症中小指展肌的收缩特性
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):894-9. doi: 10.1136/jnnp.37.8.894.
2
An analysis of myotonia in paramyotonia congenita.先天性副肌强直症中肌强直的分析。
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
3
Electromyographic distinction between paramyotonia congenita and myotonia congenita: effect of cold.先天性副肌强直症与先天性肌强直症的肌电图鉴别:寒冷的影响
Neurology. 1982 Aug;32(8):827-32. doi: 10.1212/wnl.32.8.827.
4
Influence of temperature on isometric contraction and passive muscular tension in paramyotonia congenita (Eulenburg).温度对先天性副肌强直(欧伦伯格病)等长收缩及被动肌肉张力的影响
J Neurol. 1979 Sep;221(3):151-62. doi: 10.1007/BF00313046.
5
Clinical study of paramyotonia congenita with and without myotonia in a warm environment.先天性副肌强直在温暖环境下伴或不伴肌强直的临床研究
Muscle Nerve. 1981 Sep-Oct;4(5):388-95. doi: 10.1002/mus.880040507.
6
Exercise-induced membrane failure in paramyotonia congenita.先天性副肌强直症中的运动诱导性膜衰竭
Neurology. 1986 Jan;36(1):130-2. doi: 10.1212/wnl.36.1.130.
7
Isometric contraction of the abductor digiti minimi muscle in man.人小指展肌的等长收缩。
J Neurol Neurosurg Psychiatry. 1974 Jul;37(7):825-34. doi: 10.1136/jnnp.37.7.825.
8
Muscular paralysis in myotonia congenita.先天性肌强直中的肌肉麻痹。
Eur Neurol. 1972;7(4):221-7. doi: 10.1159/000114428.
9
Paramyotonia congenita (Eulenburg): clinical, neurophysiological and muscle biopsy observations in a Swedish family.先天性副肌强直(欧伦伯格病):对一个瑞典家族的临床、神经生理学及肌肉活检观察
Acta Neurol Scand. 1993 Jan;87(1):37-42. doi: 10.1111/j.1600-0404.1993.tb04072.x.
10
Weakness in myotonic syndromes.强直性肌营养不良综合征中的肌无力
Lancet. 1977 Sep 17;2(8038):598-601. doi: 10.1016/s0140-6736(77)91441-6.

引用本文的文献

1
An analysis of myotonia in paramyotonia congenita.先天性副肌强直症中肌强直的分析。
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
2
Influence of temperature on isometric contraction and passive muscular tension in paramyotonia congenita (Eulenburg).温度对先天性副肌强直(欧伦伯格病)等长收缩及被动肌肉张力的影响
J Neurol. 1979 Sep;221(3):151-62. doi: 10.1007/BF00313046.
3
Paramyotonia congenita. A clinical, electrophysiological and histological study of 12 patients.先天性副肌强直。12例患者的临床、电生理及组织学研究。
J Neurol. 1979 Jan 5;220(4):251-7. doi: 10.1007/BF00314149.
4
Myotonia not aggravated by cooling. Force and relaxation of the adductor pollicis in normal subjects and in myotonia as compared to paramyotonia.肌强直不因冷却而加重。与僵人综合征相比,正常受试者和肌强直患者拇内收肌的肌力和松弛情况。
J Neurol. 1977 Aug 18;216(1):9-20. doi: 10.1007/BF00312810.

本文引用的文献

1
[Clinical and metabolic study of a case of Eulenburg's congenital paramyotonie. Ultrastructural data concerning the muscle biopsy].
Rev Neurol (Paris). 1966 Aug;115(2):295-311.
2
Paramyotonia and progressive neurogenic atrophy.僵人综合征和进行性神经源性萎缩。
Neurology. 1969 Sep;19(9):909-14. doi: 10.1212/wnl.19.9.909.
3
[Electromyographic study of 2 cases of von Eulenburg's paramyotonia congenita].[两例先天性副肌强直(冯·欧伦伯格型)的肌电图研究]
Rev Neurol (Paris). 1968 Jun;118(6):536-42.
4
[Eulenburg's congenital paramyotonia. Clinical, biological, histological and ultrastructural study of a further familial case].[欧伦伯格先天性副肌强直症。另一例家族性病例的临床、生物学、组织学及超微结构研究]
Rev Neurol (Paris). 1971 Jun;124(6):439-50.
5
An analysis of myotonia in paramyotonia congenita.先天性副肌强直症中肌强直的分析。
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
6
Paramyotonia congenita (Eulenburg). Neurophysiologic studies of a case.先天性副肌强直(欧伦伯格病)。一例的神经生理学研究。
Z Neurol. 1972;203(1):13-22. doi: 10.1007/BF00316075.