先天性副肌强直症中小指展肌的收缩特性
Contractile properties of the abductor digiti minimi muscle in paramyotonia congenita.
作者信息
Burke D, Skuse N F, Lethlean A K
出版信息
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):894-9. doi: 10.1136/jnnp.37.8.894.
Abstract
In two subjects with paramyotonia congenita the isometric torque generated by the abductor digiti minimi and the surface EMG recorded over ADM decreased during prolonged or repetitive contractions, whether these were voluntarily or electrically induced. Isometric twitch times did not alter significantly during this muscle fatigue. Cooling greatly accelerated the fatiguing process. It is suggested that this local muscle weakness is due to a progressive decrease in excitability of the muscle cell membrane.
摘要
在两名患有先天性副肌强直的受试者中，小指展肌产生的等长扭矩以及在小指展肌上记录的表面肌电图在长时间或重复收缩期间均下降，无论这些收缩是自愿诱发还是电诱发的。在这种肌肉疲劳过程中等长抽搐时间没有明显改变。冷却极大地加速了疲劳过程。提示这种局部肌肉无力是由于肌细胞膜兴奋性的逐渐降低所致。
相似文献
1
Contractile properties of the abductor digiti minimi muscle in paramyotonia congenita.
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):894-9. doi: 10.1136/jnnp.37.8.894.
2
An analysis of myotonia in paramyotonia congenita.
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
3
Electromyographic distinction between paramyotonia congenita and myotonia congenita: effect of cold.
Neurology. 1982 Aug;32(8):827-32. doi: 10.1212/wnl.32.8.827.
4
Influence of temperature on isometric contraction and passive muscular tension in paramyotonia congenita (Eulenburg).
J Neurol. 1979 Sep;221(3):151-62. doi: 10.1007/BF00313046.
5
Clinical study of paramyotonia congenita with and without myotonia in a warm environment.
Muscle Nerve. 1981 Sep-Oct;4(5):388-95. doi: 10.1002/mus.880040507.
6
Exercise-induced membrane failure in paramyotonia congenita.
Neurology. 1986 Jan;36(1):130-2. doi: 10.1212/wnl.36.1.130.
7
Isometric contraction of the abductor digiti minimi muscle in man.
J Neurol Neurosurg Psychiatry. 1974 Jul;37(7):825-34. doi: 10.1136/jnnp.37.7.825.
8
Muscular paralysis in myotonia congenita.
Eur Neurol. 1972;7(4):221-7. doi: 10.1159/000114428.
9
Paramyotonia congenita (Eulenburg): clinical, neurophysiological and muscle biopsy observations in a Swedish family.
Acta Neurol Scand. 1993 Jan;87(1):37-42. doi: 10.1111/j.1600-0404.1993.tb04072.x.
10
Weakness in myotonic syndromes.
Lancet. 1977 Sep 17;2(8038):598-601. doi: 10.1016/s0140-6736(77)91441-6.
引用本文的文献
1
An analysis of myotonia in paramyotonia congenita.
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
2
Influence of temperature on isometric contraction and passive muscular tension in paramyotonia congenita (Eulenburg).
J Neurol. 1979 Sep;221(3):151-62. doi: 10.1007/BF00313046.
3
Paramyotonia congenita. A clinical, electrophysiological and histological study of 12 patients.
J Neurol. 1979 Jan 5;220(4):251-7. doi: 10.1007/BF00314149.
4
Myotonia not aggravated by cooling. Force and relaxation of the adductor pollicis in normal subjects and in myotonia as compared to paramyotonia.
J Neurol. 1977 Aug 18;216(1):9-20. doi: 10.1007/BF00312810.
本文引用的文献
1
[Clinical and metabolic study of a case of Eulenburg's congenital paramyotonie. Ultrastructural data concerning the muscle biopsy].
Rev Neurol (Paris). 1966 Aug;115(2):295-311.
2
Paramyotonia and progressive neurogenic atrophy.
Neurology. 1969 Sep;19(9):909-14. doi: 10.1212/wnl.19.9.909.
3
[Electromyographic study of 2 cases of von Eulenburg's paramyotonia congenita].
Rev Neurol (Paris). 1968 Jun;118(6):536-42.
4
[Eulenburg's congenital paramyotonia. Clinical, biological, histological and ultrastructural study of a further familial case].
Rev Neurol (Paris). 1971 Jun;124(6):439-50.
5
An analysis of myotonia in paramyotonia congenita.
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
6
Paramyotonia congenita (Eulenburg). Neurophysiologic studies of a case.
Z Neurol. 1972;203(1):13-22. doi: 10.1007/BF00316075.
Zotero 插件