先天性副肌强直症中肌强直的分析。
An analysis of myotonia in paramyotonia congenita.
作者信息
Burke D, Skuse N F, Lethlean A K
出版信息
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):900-6. doi: 10.1136/jnnp.37.8.900.
Abstract
In two subjects with paramyotonia congenita myotonic delay in muscle relaxation, recorded electromyographically and with a displacement transducer, was found to increase with repeated forceful contractions. Myotonia was elicited readily in warm temperatures, was initially aggravated by cooling, but was invariably lost as muscle fatigue developed. The EMG evidence of myotonia usually subsided before complete muscle relaxation had occurred, suggesting that a defect of the contractile mechanism was present over and above any defect at membrane level.
摘要
在两名先天性副肌强直患者中，通过肌电图和位移传感器记录发现，肌肉放松时的肌强直延迟会随着反复强力收缩而增加。在温暖温度下很容易诱发肌强直，最初会因冷却而加重，但随着肌肉疲劳的发展最终会消失。肌强直的肌电图证据通常在肌肉完全放松之前就会消退，这表明除了膜水平的任何缺陷之外，收缩机制也存在缺陷。
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引用本文的文献
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Contractile properties of the abductor digiti minimi muscle in paramyotonia congenita.先天性副肌强直症中小指展肌的收缩特性
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):894-9. doi: 10.1136/jnnp.37.8.894.
2
Influence of temperature on isometric contraction and passive muscular tension in paramyotonia congenita (Eulenburg).温度对先天性副肌强直（欧伦伯格病）等长收缩及被动肌肉张力的影响
J Neurol. 1979 Sep;221(3):151-62. doi: 10.1007/BF00313046.
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J Neurol. 1979 Jan 5;220(4):251-7. doi: 10.1007/BF00314149.
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Contractile properties of the abductor digiti minimi muscle in paramyotonia congenita.先天性副肌强直症中小指展肌的收缩特性
J Neurol Neurosurg Psychiatry. 1974 Aug;37(8):894-9. doi: 10.1136/jnnp.37.8.894.
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