Meyer J J, Sane S M, Drake R M
Pediatrics. 1979 Jun;63(6):879-85.
A rare case of malignant paraganglioma of the urinary bladder with metastasis to a lymph node in a 12-year-old girl is reported, and eight other previously recorded cases are reviewed. Headache, fainting, and hypertension initiated by voiding were the most prominent clinical symptoms. Hematuria was present in three cases and aided in prompt diagnosis. Cystography, pelvic angiography, and cystoscopy were most diagnostic. Segmental cystectomy when feasible, was the preferred surgical treatment. The prognosis was slightly better than for other forms of extraadrenal pheochromocytomas.
报告了一例12岁女孩膀胱恶性副神经节瘤伴淋巴结转移的罕见病例,并回顾了其他8例既往记录的病例。排尿引发的头痛、昏厥和高血压是最突出的临床症状。3例出现血尿,有助于早期诊断。膀胱造影、盆腔血管造影和膀胱镜检查最具诊断价值。可行时,节段性膀胱切除术是首选的手术治疗方法。其预后略优于其他形式的肾上腺外嗜铬细胞瘤。